HMGA2

high mobility group AT-hook 2

Summary

This gene encodes a protein that belongs to the non-histone chromosomal high mobility group (HMG) protein family. HMG proteins function as architectural factors and are essential components of the enhancesome. This protein contains structural DNA-binding domains and may act as a transcriptional regulating factor. Identification of the deletion, amplification, and rearrangement of this gene that are associated with myxoid liposarcoma suggests a role in adipogenesis and mesenchymal differentiation. A gene knock out study of the mouse counterpart demonstrated that this gene is involved in diet-induced obesity. Alternate transcriptional splice variants, encoding different isoforms, have been characterized. [provided by RefSeq, Jul 2008]

Known Variants49 total

rsidPosition (GRCh37)AllelesClassClinVar
rs207080812:66,217,872T/C
rs53795054312:66,218,799C/T
rs144843264412:66,219,065T/Glikely benign
rs249892997412:66,219,167T/Auncertain significance
rs187029723812:66,221,823C/Tuncertain significance
rs111416731912:66,221,862C/Tpathogenic
rs124158610812:66,221,868G/Auncertain significance
rs146012112:66,222,152C/G
rs227204612:66,224,461A/Cregulatory region variant
rs797967312:66,227,257C/Tintron variant
rs5567463012:66,232,291A/Glikely benign
rs148305410312:66,232,312C/Tuncertain significance
rs117341674812:66,232,323C/Tuncertain significance
rs74842965712:66,232,331A/Glikely benign
rs258393412:66,232,810G/A
rs261205912:66,239,111A/T
rs1087833912:66,239,874A/Gregulatory region variant
rs11625712612:66,245,053G/Adownstream gene variant
rs11800350012:66,245,955G/Adownstream gene variant
rs34309312:66,255,005G/T
rs56779639912:66,272,780T/C
rs57128705312:66,282,645G/A
rs74553968812:66,308,674C/Tlikely benign
rs249906833112:66,308,861G/Auncertain significance
rs7797091912:66,308,896A/Gbenign
rs230643612:66,308,915T/Cbenign
rs1117596712:66,321,344C/Gupstream gene variant
rs1117596812:66,321,633A/G
rs499284612:66,327,028C/Tdownstream gene variant
rs1087834912:66,327,632A/T
rs1281075812:66,328,027C/Tdownstream gene variant
rs1710192312:66,338,202G/Tregulatory region variant
rs103819612:66,343,400G/A
rs1078450212:66,343,810C/Tregulatory region variant
rs15101778612:66,345,187C/Glikely benign
rs57765478412:66,345,204T/Clikely benign
rs14243294212:66,346,128C/Tlikely benign
rs7409783312:66,346,207T/Cbenign
rs187167412:66,348,134T/Aintron variant
rs1717967012:66,349,812A/Gintron variant
rs135139412:66,351,826T/G
rs1117598012:66,352,572C/Tregulatory region variant
rs159247111212:66,357,023A/Guncertain significance
rs14388069212:66,357,042A/Tlikely benign
rs249913624412:66,357,053A/Guncertain significance
rs20186092312:66,357,057T/Clikely benign
rs77200026912:66,357,073G/Alikely benign
rs104272512:66,358,347C/T3 prime UTR variant
rs875612:66,359,752C/G

Gene information from NCBI Gene. Variant classifications from ClinVar.