PITX2
paired like homeodomain 2
Summary
This gene encodes a member of the RIEG/PITX homeobox family, which is in the bicoid class of homeodomain proteins. The encoded protein acts as a transcription factor and regulates procollagen lysyl hydroxylase gene expression. This protein plays a role in the terminal differentiation of somatotroph and lactotroph cell phenotypes, is involved in the development of the eye, tooth and abdominal organs, and acts as a transcriptional regulator involved in basal and hormone-regulated activity of prolactin. Mutations in this gene are associated with Axenfeld-Rieger syndrome, iridogoniodysgenesis syndrome, and sporadic cases of Peters anomaly. A similar protein in other vertebrates is involved in the determination of left-right asymmetry during development. Alternatively spliced transcript variants encoding distinct isoforms have been described. [provided by RefSeq, Jul 2008]
Known Variants178 total
| rsid | Position (GRCh37) | Alleles | Class | ClinVar |
|---|---|---|---|---|
| rs1728803615 | 4:111,538,585 | T/G | — | uncertain significance |
| rs185925533 | 4:111,538,594 | T/C | — | uncertain significance |
| rs886059002 | 4:111,538,670 | T/C | — | uncertain significance |
| rs886059003 | 4:111,538,709 | A/G | — | uncertain significance |
| rs188349821 | 4:111,538,759 | A/G | — | uncertain significance |
| rs75911264 | 4:111,538,810 | C/T | — | likely benign |
| rs6533526 | 4:111,538,827 | G/A | upstream gene variant | benign |
| rs1301785358 | 4:111,538,841 | G/A | — | uncertain significance |
| rs886059005 | 4:111,538,911 | C/G | — | uncertain significance |
| rs551209662 | 4:111,538,941 | T/C | — | conflicting classifications of pathogenicity |
| rs886059006 | 4:111,539,017 | T/G | — | uncertain significance |
| rs567517676 | 4:111,539,105 | T/A | — | uncertain significance |
| rs1728830475 | 4:111,539,108 | C/T | — | uncertain significance |
| rs765040142 | 4:111,539,162 | A/T | — | uncertain significance |
| rs752553102 | 4:111,539,174 | T/G | — | uncertain significance |
| rs2476648826 | 4:111,539,298 | C/T | — | uncertain significance |
| rs571758306 | 4:111,539,315 | C/T | — | uncertain significance |
| rs1728842390 | 4:111,539,327 | G/T | — | uncertain significance |
| rs1490127358 | 4:111,539,329 | C/T | — | likely benign |
| rs760790139 | 4:111,539,340 | C/T | — | uncertain significance |
| rs1184603292 | 4:111,539,354 | A/C | — | uncertain significance |
| rs139401187 | 4:111,539,394 | G/A | — | conflicting classifications of pathogenicity |
| rs148191851 | 4:111,539,437 | C/T | — | likely benign |
| rs778779105 | 4:111,539,440 | C/T | — | likely benign |
| rs371238455 | 4:111,539,444 | T/A | — | uncertain significance |
| rs1057519489 | 4:111,539,449 | A/T | stop gained | pathogenic |
| rs145355581 | 4:111,539,461 | C/A | — | likely benign |
| rs1057519488 | 4:111,539,471 | — | — | pathogenic |
| rs146807994 | 4:111,539,528 | C/T | — | uncertain significance |
| rs1336888015 | 4:111,539,559 | T/C | — | uncertain significance |
| rs746908680 | 4:111,539,561 | C/T | — | uncertain significance |
| rs748391268 | 4:111,539,575 | C/T | — | uncertain significance |
| rs760018349 | 4:111,539,600 | G/C | — | uncertain significance |
| rs763539767 | 4:111,539,605 | C/G | — | uncertain significance |
| rs141176394 | 4:111,539,617 | T/A | — | conflicting classifications of pathogenicity |
| rs761378970 | 4:111,539,622 | G/A | — | likely benign |
| rs2476652210 | 4:111,539,623 | G/A | — | likely benign |
| rs893139859 | 4:111,539,625 | G/T | — | uncertain significance |
| rs138163892 | 4:111,539,637 | T/C | — | conflicting classifications of pathogenicity |
| rs35946364 | 4:111,539,638 | A/C | — | likely benign |
| rs2110431786 | 4:111,539,664 | T/A | — | likely benign |
| rs749452484 | 4:111,539,668 | T/G | — | likely benign |
| rs193920830 | 4:111,539,676 | C/T | — | uncertain significance |
| rs77144743 | 4:111,539,694 | C/T | — | likely benign |
| rs104893860 | 4:111,539,698 | C/T | stop gained | pathogenic |
| rs2476656626 | 4:111,539,699 | C/T | — | pathogenic |
| rs2476656732 | 4:111,539,705 | T/C | — | uncertain significance |
| rs1578446544 | 4:111,539,722 | G/C | — | pathogenic |
| rs951710742 | 4:111,539,734 | G/C | — | pathogenic |
| rs1728874429 | 4:111,539,739 | G/A | — | uncertain significance |
| rs752617007 | 4:111,539,761 | C/A | — | likely benign |
| rs756196786 | 4:111,539,767 | G/A | — | likely benign |
| rs1057519486 | 4:111,539,823 | C/G | — | uncertain significance |
| rs104893859 | 4:111,539,825 | C/G | missense variant | pathogenic |
| rs1057519485 | 4:111,539,826 | G/A | — | likely pathogenic |
| rs769461476 | 4:111,539,827 | A/T | — | likely benign |
| rs2476658099 | 4:111,539,828 | C/G | — | pathogenic |
| rs2476658116 | 4:111,539,831 | T/C | — | uncertain significance |
| rs387906810 | 4:111,539,835 | T/C | missense variant | pathogenic |
| rs2476658147 | 4:111,539,838 | A/G | — | likely pathogenic |
| rs2476658161 | 4:111,539,839 | C/A | — | pathogenic |
| rs772800095 | 4:111,539,840 | C/G | — | pathogenic |
| rs2476658214 | 4:111,539,845 | C/T | — | pathogenic |
| rs1553922583 | 4:111,539,846 | T/A | — | pathogenic |
| rs762349019 | 4:111,539,851 | G/A | — | uncertain significance |
| rs1198152064 | 4:111,539,855 | T/C | — | pathogenic |
| rs56075507 | 4:111,539,946 | C/T | — | likely benign |
| rs143597654 | 4:111,540,115 | A/G | — | likely benign |
| rs1322668139 | 4:111,540,127 | G/T | — | uncertain significance |
| rs146850335 | 4:111,542,095 | G/A | — | likely benign |
| rs2278783 | 4:111,542,124 | G/A | — | benign |
| rs2278782 | 4:111,542,154 | G/A | — | benign |
| rs1560590094 | 4:111,542,315 | C/G | — | pathogenic |
| rs1578450728 | 4:111,542,318 | A/C | — | pathogenic |
| rs1728998905 | 4:111,542,319 | C/T | — | pathogenic |
| rs121909248 | 4:111,542,322 | G/A | missense variant | pathogenic |
| rs121909249 | 4:111,542,325 | C/G | missense variant | pathogenic |
| rs2529772641 | 4:111,542,340 | G/C | — | uncertain significance |
| rs1729000479 | 4:111,542,342 | T/C | — | uncertain significance |
| rs2529772680 | 4:111,542,347 | C/T | — | pathogenic |
| rs1729000976 | 4:111,542,348 | C/T | — | pathogenic |
| rs2110435645 | 4:111,542,355 | C/G | — | pathogenic |
| rs104893861 | 4:111,542,366 | C/T | missense variant | pathogenic |
| rs104893858 | 4:111,542,370 | T/G | missense variant | pathogenic |
| rs1057519484 | 4:111,542,381 | G/A | missense variant | pathogenic |
| rs104893862 | 4:111,542,387 | C/T | missense variant | pathogenic |
| rs1729003669 | 4:111,542,399 | A/G | — | likely pathogenic |
| rs104893857 | 4:111,542,411 | A/T | missense variant | pathogenic |
| rs1051887 | 4:111,542,415 | C/A | — | pathogenic |
| rs2529773049 | 4:111,542,423 | T/C | — | likely pathogenic |
| rs1553922901 | 4:111,542,424 | G/A | — | pathogenic |
| rs2529773099 | 4:111,542,435 | A/G | — | likely pathogenic |
| rs1729005855 | 4:111,542,442 | T/G | — | uncertain significance |
| rs2110435742 | 4:111,542,445 | G/A | — | pathogenic |
| rs768386257 | 4:111,542,449 | C/A | — | uncertain significance |
| rs149288560 | 4:111,542,458 | C/T | — | conflicting classifications of pathogenicity |
| rs28936409 | 4:111,542,459 | C/T | missense variant | — |
| rs1231505078 | 4:111,542,474 | G/A | — | uncertain significance |
| rs765382079 | 4:111,542,481 | C/A | — | pathogenic |
| rs1729009192 | 4:111,542,489 | A/C | — | uncertain significance |
Showing 100 of 178 variants. Use the SNP search for the full list.
Gene information from NCBI Gene. Variant classifications from ClinVar.