AANAT

aralkylamine N-acetyltransferase

Summary

The protein encoded by this gene belongs to the acetyltransferase superfamily. It is the penultimate enzyme in melatonin synthesis and controls the night/day rhythm in melatonin production in the vertebrate pineal gland. Melatonin is essential for the function of the circadian clock that influences activity and sleep. This enzyme is regulated by cAMP-dependent phosphorylation that promotes its interaction with 14-3-3 proteins and thus protects the enzyme against proteasomal degradation. This gene may contribute to numerous genetic diseases such as delayed sleep phase syndrome. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2009]

Known Variants27 total

rsidPosition (GRCh37)AllelesClassClinVar
rs376013817:74,463,109G/Tdownstream gene variant
rs423898917:74,463,388C/Gdownstream gene variant
rs6173939517:74,464,836C/Tbenign
rs14100626217:74,464,914G/Alikely benign
rs13976536917:74,464,920C/Tuncertain significance
rs75452192917:74,464,982G/Cuncertain significance
rs250974909017:74,465,258T/Cuncertain significance
rs77789354217:74,465,303G/Auncertain significance
rs14643040517:74,465,321G/Auncertain significance
rs86725522317:74,465,389G/Cuncertain significance
rs74938285817:74,465,393A/Guncertain significance
rs117073951517:74,465,405T/Auncertain significance
rs14019492017:74,465,794T/Clikely benign
rs15035756717:74,465,811G/Auncertain significance
rs20046828417:74,465,812C/Tlikely benign
rs2893667917:74,465,813G/Amissense variantuncertain significance
rs97070868217:74,465,819C/Tuncertain significance
rs74787274817:74,465,820G/Auncertain significance
rs55389229117:74,465,853G/Auncertain significance
rs128667278017:74,465,894G/Cuncertain significance
rs207103117:74,465,896C/Tbenign
rs14387424017:74,465,909G/Auncertain significance
rs77352801617:74,465,912G/Auncertain significance
rs78000224317:74,465,942A/Tuncertain significance
rs5850410417:74,465,971C/Abenign
rs15088141217:74,465,984C/Tuncertain significance
rs75415855717:74,465,987A/Glikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.