ACAA2

acetyl-CoA acyltransferase 2

Summary

The encoded protein catalyzes the last step of the mitochondrial fatty acid beta-oxidation spiral. Unlike most mitochondrial matrix proteins, it contains a non-cleavable amino-terminal targeting signal. [provided by RefSeq, Jul 2008]

Known Variants26 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14221191518:47,310,279C/Guncertain significance
rs75363101618:47,310,290C/Guncertain significance
rs37179312918:47,310,296C/Auncertain significance
rs77101252818:47,310,300G/Auncertain significance
rs74586590418:47,311,574C/Tuncertain significance
rs251136524418:47,311,615A/Tuncertain significance
rs53903688018:47,313,679C/Guncertain significance
rs124868135918:47,317,843T/Cuncertain significance
rs251136787018:47,317,923G/Cuncertain significance
rs37753210318:47,317,966C/Tlikely benign
rs77083476318:47,318,563C/Tuncertain significance
rs74778365218:47,318,625A/Guncertain significance
rs13893241018:47,318,659T/Cuncertain significance
rs14943692018:47,318,683A/Tbenign
rs76369399418:47,320,680C/Tuncertain significance
rs37183466218:47,320,782A/Guncertain significance
rs251136985018:47,322,154T/Guncertain significance
rs20085996418:47,322,179C/Tuncertain significance
rs75724860118:47,322,184T/Cuncertain significance
rs19950447418:47,322,238T/Cuncertain significance
rs18371643818:47,326,426C/A
rs54462840518:47,326,672G/T
rs14653527718:47,329,070C/Auncertain significance
rs76541517218:47,329,098G/Tuncertain significance
rs251137350218:47,329,146A/Cuncertain significance
rs37435528318:47,329,157G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.