ACSS1

acyl-CoA synthetase short chain family member 1

Summary

This gene encodes a mitochondrial acetyl-CoA synthetase enzyme. A similar protein in mice plays an important role in the tricarboxylic acid cycle by catalyzing the conversion of acetate to acetyl CoA. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Nov 2011]

Known Variants42 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14389071220:24,988,454C/Tlikely benign
rs20127944020:24,988,462C/Guncertain significance
rs77186403920:24,988,466G/Auncertain significance
rs77032749320:24,988,483G/Auncertain significance
rs77529542920:24,988,507C/Auncertain significance
rs57500573320:24,989,958T/Clikely benign
rs54069407620:24,989,991G/Auncertain significance
rs103788633420:24,990,006A/Cuncertain significance
rs56582984320:24,993,238T/Auncertain significance
rs37094979820:24,993,480G/Auncertain significance
rs208843855920:24,993,560C/Tuncertain significance
rs132576105120:24,994,195T/Cuncertain significance
rs74703118920:24,994,204C/Auncertain significance
rs36767099220:24,994,274C/Tuncertain significance
rs11268386520:24,994,614C/Tbenign
rs77501655820:24,994,689C/Tuncertain significance
rs13814103620:25,000,679A/Guncertain significance
rs14567943220:25,000,683C/Tbenign
rs125113705820:25,000,717C/Tuncertain significance
rs251493391620:25,002,087C/Guncertain significance
rs37187883820:25,003,590C/Tuncertain significance
rs4131509620:25,003,597G/Csynonymous variant
rs14471439120:25,003,701C/Tuncertain significance
rs37546946920:25,004,112G/Auncertain significance
rs14048386820:25,004,176C/Tuncertain significance
rs55318574920:25,004,248G/Cuncertain significance
rs7767125320:25,005,088G/Tintron variant
rs7665907720:25,005,602T/Cintron variant
rs6221717520:25,005,948T/Cintron variant
rs18822887320:25,008,915A/Gintron variant
rs57162019020:25,010,172A/T
rs96537429320:25,011,446C/Tuncertain significance
rs20065089520:25,011,506C/Tuncertain significance
rs251496146420:25,011,592T/Cuncertain significance
rs75855386020:25,013,019G/Alikely benign
rs18199064020:25,015,390G/Cintron variant
rs605026720:25,019,099G/Aintron variant
rs14843420620:25,028,758G/Auncertain significance
rs11359872920:25,028,776C/Tlikely benign
rs251502547120:25,038,607G/Tuncertain significance
rs104601775020:25,038,643G/Tuncertain significance
rs98761064120:25,038,651C/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.