ACSS2

acyl-CoA synthetase short chain family member 2

Summary

This gene encodes a cytosolic enzyme that catalyzes the activation of acetate for use in lipid synthesis and energy generation. The protein acts as a monomer and produces acetyl-CoA from acetate in a reaction that requires ATP. Expression of this gene is regulated by sterol regulatory element-binding proteins, transcription factors that activate genes required for the synthesis of cholesterol and unsaturated fatty acids. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2009]

Known Variants57 total

rsidPosition (GRCh37)AllelesClassClinVar
rs138885497520:33,464,478C/Guncertain significance
rs74748687720:33,464,528G/Cuncertain significance
rs77138897320:33,464,534G/Cuncertain significance
rs251877171820:33,464,569G/Auncertain significance
rs14648610420:33,464,572C/Abenign
rs98438060420:33,464,582A/Guncertain significance
rs76413947420:33,464,603G/Cuncertain significance
rs6037940520:33,470,659C/Tuncertain significance
rs5703185220:33,470,660G/Alikely benign
rs76878474920:33,470,663A/Tuncertain significance
rs124302218320:33,470,698G/Auncertain significance
rs812321020:33,486,047G/T
rs6771950820:33,487,278T/Cintron variant
rs378721520:33,493,877A/T
rs128600358220:33,500,935A/Glikely benign
rs126660890220:33,500,969A/Guncertain significance
rs37772649320:33,501,230G/Auncertain significance
rs11201277720:33,501,271C/Tuncertain significance
rs14383204620:33,501,583T/Cuncertain significance
rs14816608720:33,501,946G/Cuncertain significance
rs6101466720:33,502,162C/Tbenign
rs20104116920:33,502,170G/Auncertain significance
rs78014078820:33,502,211C/Auncertain significance
rs117516171520:33,502,214A/Glikely benign
rs77649207720:33,503,031A/Tuncertain significance
rs6135911320:33,507,301T/Abenign
rs5709222320:33,507,324C/Tlikely benign
rs18097904020:33,507,325G/Auncertain significance
rs37054485220:33,507,330C/Tlikely benign
rs5912680520:33,508,358T/Cbenign
rs6086784720:33,508,395G/Alikely benign
rs125076748020:33,508,457C/Tuncertain significance
rs20141813920:33,508,471G/Auncertain significance
rs37695055720:33,508,887A/Guncertain significance
rs5884594920:33,508,906G/Auncertain significance
rs251897192920:33,508,927A/Tuncertain significance
rs93492560520:33,509,141G/Auncertain significance
rs156899887520:33,509,214G/Clikely benign
rs14406138020:33,509,221G/Tuncertain significance
rs77903870620:33,509,366C/Guncertain significance
rs20062849820:33,509,377G/Auncertain significance
rs251897526720:33,509,384C/Auncertain significance
rs5831441320:33,509,394C/Tlikely benign
rs74668544320:33,509,395G/Auncertain significance
rs5908848520:33,509,608T/Cuncertain significance
rs251897702720:33,509,626A/Guncertain significance
rs37265281520:33,509,640G/Auncertain significance
rs5911644220:33,509,655G/Auncertain significance
rs76871902420:33,513,501G/Cuncertain significance
rs14251371820:33,513,939A/Gbenign
rs124284953620:33,513,955G/Auncertain significance
rs76704138020:33,514,003G/Auncertain significance
rs140677751020:33,514,039G/Auncertain significance
rs5873588120:33,514,065C/Tlikely benign
rs18838212820:33,514,221C/Adownstream gene variant
rs75430324620:33,514,701T/Cuncertain significance
rs208133903220:33,514,992G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.