ADAMTS8

ADAM metallopeptidase with thrombospondin type 1 motif 8

Summary

This gene encodes a member of the ADAMTS (a disintegrin and metalloproteinase with thrombospondin motifs) protein family. Members of the family share several distinct protein modules, including a propeptide region, a metalloproteinase domain, a disintegrin-like domain, and a thrombospondin type 1 (TS) motif. Individual members of this family differ in the number of C-terminal TS motifs, and some have unique C-terminal domains. The encoded preproprotein is proteolytically processed to generate the mature enzyme. This enzyme contains two C-terminal TS motifs, and disrupts angiogenesis in vivo. A number of disorders have been mapped in the vicinity of this gene, most notably lung neoplasms. Reduced expression of this gene has been observed in multiple human cancers and this gene has been proposed as a potential tumor suppressor. [provided by RefSeq, Feb 2016]

Known Variants69 total

rsidPosition (GRCh37)AllelesClassClinVar
rs74904668711:130,275,554C/Guncertain significance
rs77066672011:130,275,559C/Tuncertain significance
rs19962617311:130,275,572C/Tuncertain significance
rs76890986711:130,275,578C/Tuncertain significance
rs254148416711:130,275,600C/Guncertain significance
rs37386010911:130,275,724G/Tuncertain significance
rs37463039611:130,275,785G/Auncertain significance
rs76037480811:130,275,799C/Tuncertain significance
rs145926699611:130,275,821C/Tuncertain significance
rs90590963211:130,275,826T/Cuncertain significance
rs74601417511:130,275,961C/Tuncertain significance
rs74729223811:130,275,971C/Tuncertain significance
rs19976038211:130,276,014G/Tuncertain significance
rs18073241311:130,276,196A/Cintron variant
rs76802756111:130,278,411C/Tuncertain significance
rs77553690411:130,278,671C/Tuncertain significance
rs54404087611:130,278,727C/Tuncertain significance
rs3482140711:130,278,728G/Auncertain significance
rs254148768011:130,278,749T/Cuncertain significance
rs6175485111:130,278,773C/Tmissense variant
rs793692811:130,279,168T/Cintron variant
rs37559121311:130,281,411G/Auncertain significance
rs254149022111:130,281,412G/Tuncertain significance
rs5579693911:130,284,041C/A
rs127378948711:130,284,479G/Auncertain significance
rs254149331111:130,284,481C/Tuncertain significance
rs78044321411:130,284,488C/Tuncertain significance
rs53874066011:130,284,493G/Auncertain significance
rs77270522411:130,284,500C/Tuncertain significance
rs76210875211:130,284,529G/Auncertain significance
rs254149343011:130,284,538A/Cuncertain significance
rs57434691111:130,284,543C/Tlikely benign
rs105508543611:130,284,554C/Tuncertain significance
rs77037830511:130,284,575C/Tuncertain significance
rs144724654011:130,284,592G/Cuncertain significance
rs75697969911:130,284,635T/Cuncertain significance
rs144397263311:130,284,647C/Tuncertain significance
rs3612491711:130,284,668G/Amissense variant
rs74711392211:130,286,064C/Tuncertain significance
rs75910919611:130,286,090A/Guncertain significance
rs37101850311:130,286,886C/Tuncertain significance
rs37560774511:130,286,928C/Tuncertain significance
rs75941767211:130,288,970G/Auncertain significance
rs229134811:130,289,117T/Cmissense variant
rs146556729111:130,289,136T/Cuncertain significance
rs19951317211:130,289,168A/Guncertain significance
rs78089904111:130,289,186T/Cuncertain significance
rs37503586411:130,297,470C/Tuncertain significance
rs143909782711:130,297,476C/Tuncertain significance
rs37197706211:130,297,559G/Cuncertain significance
rs77380324311:130,297,610T/Guncertain significance
rs155507567711:130,297,614T/Clikely benign
rs75243737311:130,297,629C/Tuncertain significance
rs122471305011:130,297,719G/Auncertain significance
rs144866971711:130,297,742G/Auncertain significance
rs78147091711:130,297,812C/Tuncertain significance
rs103783928811:130,297,890G/Cuncertain significance
rs140977567511:130,297,928C/Guncertain significance
rs77856286411:130,297,958A/Tuncertain significance
rs75783685911:130,297,976G/Auncertain significance
rs77914027011:130,297,977C/Auncertain significance
rs75798677611:130,297,990G/Tuncertain significance
rs76813449311:130,297,996C/Guncertain significance
rs77238636411:130,298,036C/Tuncertain significance
rs115719465811:130,298,078C/Tuncertain significance
rs141161410411:130,298,082C/Auncertain significance
rs100369071211:130,298,147G/Auncertain significance
rs254150931711:130,298,169G/Auncertain significance
rs7304482011:130,300,152C/Aupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.