AKR1C1

aldo-keto reductase family 1 member C1

Summary

This gene encodes a member of the aldo/keto reductase superfamily, which consists of more than 40 known enzymes and proteins. These enzymes catalyze the conversion of aldehydes and ketones to their corresponding alcohols by utilizing NADH and/or NADPH as cofactors. The enzymes display overlapping but distinct substrate specificity. This enzyme catalyzes the reaction of progesterone to the inactive form 20-alpha-hydroxy-progesterone. This gene shares high sequence identity with three other gene members and is clustered with those three genes at chromosome 10p15-p14. [provided by RefSeq, Jul 2008]

Known Variants34 total

rsidPosition (GRCh37)AllelesClassClinVar
rs77118828310:5,005,644C/Tuncertain significance
rs78120059410:5,005,710C/Tuncertain significance
rs75561371210:5,005,712C/Tuncertain significance
rs4130566110:5,005,860G/Tregulatory region variant
rs707373810:5,006,098G/Aupstream gene variant
rs156431473510:5,008,131C/Guncertain significance
rs14642846610:5,008,140T/Glikely benign
rs76858263510:5,008,149A/Tuncertain significance
rs14929564410:5,008,183A/Tuncertain significance
rs37575258310:5,009,138G/Cuncertain significance
rs76459933810:5,009,141C/Guncertain significance
rs14096691110:5,009,188T/Cbenign
rs77890343810:5,009,216A/Cuncertain significance
rs14564889410:5,009,739T/Gupstream gene variant
rs290480410:5,009,759G/C
rs113860010:5,010,572A/Glikely benign
rs77407374510:5,011,072A/Guncertain significance
rs14981401010:5,011,074C/Tuncertain significance
rs37361744010:5,014,408T/Cuncertain significance
rs249129555510:5,014,415A/Guncertain significance
rs78250566210:5,014,438T/Guncertain significance
rs78218689210:5,014,501T/Cuncertain significance
rs78210146010:5,014,792C/Tuncertain significance
rs117644405310:5,014,813G/Tuncertain significance
rs142256793910:5,014,822G/Tuncertain significance
rs14039630610:5,014,844G/Auncertain significance
rs78256612110:5,014,845A/Clikely benign
rs20122958610:5,014,855C/Guncertain significance
rs249129654110:5,014,920G/Tuncertain significance
rs78197384410:5,014,922G/Tuncertain significance
rs14220084010:5,014,935C/Abenign
rs117294106710:5,019,906C/Tuncertain significance
rs5613618110:5,020,919C/T3 prime UTR variant
rs660188810:5,025,639T/A

Gene information from NCBI Gene. Variant classifications from ClinVar.