AKR1C3

aldo-keto reductase family 1 member C3

Summary

This gene encodes a member of the aldo/keto reductase superfamily, which consists of more than 40 known enzymes and proteins. These enzymes catalyze the conversion of aldehydes and ketones to their corresponding alcohols by utilizing NADH and/or NADPH as cofactors. The enzymes display overlapping but distinct substrate specificity. This enzyme catalyzes the reduction of prostaglandin (PG) D2, PGH2 and phenanthrenequinone (PQ), and the oxidation of 9alpha,11beta-PGF2 to PGD2. It may play an important role in the pathogenesis of allergic diseases such as asthma, and may also have a role in controlling cell growth and/or differentiation. This gene shares high sequence identity with three other gene members and is clustered with those three genes at chromosome 10p15-p14. Three transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Dec 2011]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs452511910:5,091,954C/Tupstream gene variant
rs747867010:5,125,538T/G
rs193784510:5,136,148A/Gupstream gene variant
rs1252910:5,136,651C/Gmissense variant
rs19392084210:5,136,663G/Tuncertain significance
rs155478486310:5,136,684G/Alikely benign
rs251804910:5,138,036A/Gregulatory region variant
rs15075354210:5,138,656C/Tuncertain significance
rs78219085510:5,138,711T/Guncertain significance
rs3596189410:5,138,714G/Abenign
rs78215713810:5,138,738T/Cuncertain significance
rs20098181610:5,139,642A/Guncertain significance
rs14044189410:5,139,694A/Tuncertain significance
rs78275350010:5,141,049T/Guncertain significance
rs2894357910:5,141,058G/Abenign
rs1050829310:5,141,137A/T
rs19231453410:5,141,520C/Tuncertain significance
rs193783910:5,141,530G/Abenign
rs78217116510:5,141,572C/Guncertain significance
rs14058049810:5,141,639C/Tlikely benign
rs15122950410:5,144,306C/Tlikely benign
rs13914641110:5,144,318G/Abenign
rs53613844810:5,144,323A/Guncertain significance
rs20085890510:5,144,354T/Guncertain significance
rs48335282010:5,144,365G/Anot provided
rs155478623110:5,144,677G/Tuncertain significance
rs129361044910:5,144,727T/Guncertain significance
rs78237769510:5,144,744C/Guncertain significance
rs78226600410:5,144,808G/Auncertain significance
rs36818212910:5,144,814A/Guncertain significance
rs14061330810:5,144,822C/Tuncertain significance
rs155478630310:5,144,825A/Guncertain significance
rs147655115210:5,144,841A/Cuncertain significance
rs78214164810:5,147,842G/Cuncertain significance
rs249154920710:5,147,868A/Tuncertain significance
rs18379113710:5,150,158C/Tdownstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.