ALDH16A1

aldehyde dehydrogenase 16 family member A1

Summary

This gene encodes a member of the aldehyde dehydrogenase superfamily. The family members act on aldehyde substrates and use nicotinamide adenine dinucleotide phosphate (NADP) as a cofactor. This gene is conserved in chimpanzee, dog, cow, mouse, rat, and zebrafish. The protein encoded by this gene interacts with maspardin, a protein that when truncated is responsible for Mast syndrome. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Apr 2010]

Known Variants67 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14436200519:49,956,613C/Alikely benign
rs75116409119:49,956,616G/Cuncertain significance
rs37460244219:49,956,655C/Tuncertain significance
rs251393406219:49,961,792A/Guncertain significance
rs160102083219:49,962,310A/Tlikely benign
rs13982817219:49,962,927G/Alikely benign
rs37542414719:49,962,991C/Tuncertain significance
rs14889674319:49,963,010G/Auncertain significance
rs14191966919:49,963,021G/Auncertain significance
rs126015249519:49,964,079G/Auncertain significance
rs75261735119:49,964,105A/Guncertain significance
rs74859485419:49,964,144G/Auncertain significance
rs141683883819:49,964,150G/Tuncertain significance
rs14695792119:49,964,166G/Abenign
rs37034410319:49,964,990C/Tuncertain significance
rs74668441319:49,965,027C/Guncertain significance
rs77670415619:49,965,053C/Guncertain significance
rs76389625419:49,965,145G/Auncertain significance
rs75683097919:49,965,147C/Tuncertain significance
rs77424700319:49,965,168G/Auncertain significance
rs74594002419:49,965,169C/Auncertain significance
rs77605048019:49,965,170G/Alikely benign
rs14276473519:49,965,172G/Alikely benign
rs86588846719:49,965,181C/Guncertain significance
rs725991719:49,965,185G/Tuncertain significance
rs76628835219:49,965,186C/Auncertain significance
rs86780427319:49,965,196C/Tuncertain significance
rs251394172819:49,965,220T/Cuncertain significance
rs20220992619:49,965,227G/Tlikely benign
rs36888580219:49,965,241T/Cuncertain significance
rs75370637219:49,965,845A/Guncertain significance
rs14524230819:49,965,870C/Tuncertain significance
rs77641856119:49,965,906G/Cuncertain significance
rs142408003019:49,965,920C/Guncertain significance
rs54021147019:49,965,932G/Auncertain significance
rs141948996719:49,965,944G/Auncertain significance
rs76785162319:49,965,959G/Auncertain significance
rs75436357919:49,965,971G/Cuncertain significance
rs104270596719:49,966,000C/Guncertain significance
rs37067175319:49,967,136C/Tuncertain significance
rs77373873119:49,967,141C/Tuncertain significance
rs57663217719:49,967,402G/Auncertain significance
rs76627386019:49,967,418G/Cuncertain significance
rs77276955719:49,967,448A/Guncertain significance
rs37509348219:49,967,690G/Cuncertain significance
rs75653491619:49,967,693T/Cuncertain significance
rs14720324019:49,967,718A/Tlikely benign
rs13899571619:49,967,907C/Tuncertain significance
rs20087307619:49,967,912C/Tlikely benign
rs14578280919:49,967,929G/Cuncertain significance
rs37221883419:49,967,995C/Tuncertain significance
rs15041481819:49,969,006C/Amissense variant
rs75894667519:49,969,009A/Tuncertain significance
rs13838367419:49,969,030G/Auncertain significance
rs78040860419:49,969,068C/Tuncertain significance
rs97883507619:49,969,425C/Tuncertain significance
rs20194112319:49,969,461C/Tuncertain significance
rs18156616819:49,969,468G/Alikely benign
rs129245967819:49,969,472G/Cuncertain significance
rs86857956019:49,969,497G/Auncertain significance
rs75905047819:49,971,666G/Auncertain significance
rs77018030719:49,971,710G/Auncertain significance
rs76678515319:49,971,731G/Cuncertain significance
rs78138336619:49,971,759A/Guncertain significance
rs251395558319:49,971,797C/Tuncertain significance
rs1188005119:49,972,822T/Aupstream gene variant
rs14703207719:49,973,632C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.