ANKRD27

ankyrin repeat domain 27

Summary

Enables guanyl-nucleotide exchange factor activity and small GTPase binding activity. Involved in endocytic recycling and negative regulation of SNARE complex assembly. Acts upstream of or within early endosome to late endosome transport. Located in several cellular components, including cytosol; endosome; and lysosome. Implicated in eosinophilic esophagitis. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants74 total

rsidPosition (GRCh37)AllelesClassClinVar
rs76739291819:33,089,146G/Cuncertain significance
rs14837575619:33,089,209T/Auncertain significance
rs76412901619:33,089,233C/Tlikely benign
rs1769289619:33,089,431G/Aintron variant
rs3454087719:33,090,271T/Cintron variant
rs133014282119:33,090,639G/Cuncertain significance
rs251316986619:33,090,674G/Auncertain significance
rs251317035619:33,090,956C/Guncertain significance
rs75874447619:33,095,183C/Tuncertain significance
rs14567654619:33,095,200C/Tuncertain significance
rs36804804019:33,095,246C/Tuncertain significance
rs76938933419:33,095,249C/Tuncertain significance
rs37294865119:33,096,838G/Auncertain significance
rs56878695119:33,096,853T/Guncertain significance
rs74628693619:33,098,633G/Auncertain significance
rs55838108119:33,098,644G/Alikely benign
rs76130780419:33,098,647C/Guncertain significance
rs19991769319:33,098,653T/Cuncertain significance
rs93994913619:33,098,659G/Auncertain significance
rs56293128819:33,098,660C/Auncertain significance
rs37716758719:33,098,674G/Auncertain significance
rs14115370619:33,098,692C/Tlikely benign
rs77153889919:33,098,699C/Tuncertain significance
rs119723073419:33,098,738T/Cuncertain significance
rs963611419:33,101,151G/Cupstream gene variant
rs13921061819:33,106,601G/Auncertain significance
rs14602556519:33,106,618G/Alikely benign
rs251318476519:33,106,677G/Cuncertain significance
rs76544250319:33,106,686C/Auncertain significance
rs38241619:33,107,938G/Aintron variant
rs77750504719:33,110,260G/Auncertain significance
rs20150041319:33,110,263C/Auncertain significance
rs14152448019:33,110,404G/Auncertain significance
rs78114536419:33,110,405A/Guncertain significance
rs20077998719:33,110,408A/Guncertain significance
rs77812057119:33,110,418C/Guncertain significance
rs1215131119:33,112,707T/Cintron variant
rs14667502619:33,113,434C/Tuncertain significance
rs76526413419:33,113,446T/Cuncertain significance
rs75623912919:33,113,491G/Auncertain significance
rs197202981919:33,113,504A/Guncertain significance
rs197202991219:33,113,507A/Guncertain significance
rs146607568419:33,113,516C/Auncertain significance
rs14448318519:33,116,817G/Auncertain significance
rs78081445819:33,116,842C/Guncertain significance
rs77673684819:33,116,844G/Auncertain significance
rs36858018419:33,116,845C/Auncertain significance
rs251319727619:33,117,731G/Cuncertain significance
rs76748091519:33,119,006T/Auncertain significance
rs251319891019:33,119,045G/Auncertain significance
rs99959511819:33,119,065C/Guncertain significance
rs251319974319:33,119,749C/Guncertain significance
rs14003450519:33,130,266G/Cuncertain significance
rs148732702919:33,130,362C/Auncertain significance
rs20193368619:33,130,374A/Guncertain significance
rs76293272019:33,131,229T/Cuncertain significance
rs86606221519:33,132,944G/Cuncertain significance
rs251321193919:33,133,022A/Guncertain significance
rs36845268819:33,133,025T/Cuncertain significance
rs20178250719:33,134,207T/Cuncertain significance
rs13867950819:33,134,216C/Guncertain significance
rs20055374919:33,134,342C/Guncertain significance
rs74621161619:33,134,350T/Cuncertain significance
rs15086429119:33,134,483G/Tuncertain significance
rs75299425619:33,135,279G/Cuncertain significance
rs74558322419:33,135,308C/Tuncertain significance
rs77360716819:33,137,430T/Cuncertain significance
rs77902462319:33,140,683T/Cuncertain significance
rs25925119:33,149,768G/Aupstream gene variant
rs74619927619:33,149,822T/Guncertain significance
rs54557697319:33,149,860C/Tuncertain significance
rs37382859819:33,154,879G/T
rs725262119:33,156,368G/C
rs25928319:33,163,103A/C

Gene information from NCBI Gene. Variant classifications from ClinVar.