ANO1

anoctamin 1

Summary

Enables identical protein binding activity; iodide transmembrane transporter activity; and ligand-gated monoatomic ion channel activity. Involved in several processes, including monoatomic anion transport; mucus secretion; and positive regulation of insulin secretion involved in cellular response to glucose stimulus. Located in apical plasma membrane and nucleoplasm. Implicated in Moyamoya disease. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants87 total

rsidPosition (GRCh37)AllelesClassClinVar
rs11353928211:69,811,698C/Tintergenic variant
rs11141275511:69,819,139C/Tintergenic variant
rs7293177911:69,833,580C/A
rs14188106011:69,842,131C/Aintron variant
rs90287511:69,860,399G/C
rs3454455711:69,911,825C/G
rs441130311:69,919,214A/Tupstream gene variant
rs36890383011:69,924,729A/Guncertain significance
rs75735126911:69,924,735C/Guncertain significance
rs19976302511:69,924,755C/Tuncertain significance
rs76594667511:69,924,803C/Guncertain significance
rs250913311:69,933,717T/Cregulatory region variant
rs36853476811:69,933,921G/Auncertain significance
rs37173961511:69,933,978C/Tuncertain significance
rs36900989311:69,933,992G/Alikely benign
rs37388095011:69,934,066C/Tuncertain significance
rs76437533211:69,934,069C/Tuncertain significance
rs37090818311:69,934,129G/Tuncertain significance
rs75793468611:69,934,180G/Cuncertain significance
rs54225987011:69,934,184C/Auncertain significance
rs19981378711:69,934,185G/Auncertain significance
rs1075109711:69,938,433A/Gintron variant
rs55071756211:69,949,178A/Guncertain significance
rs86789092311:69,949,238G/Auncertain significance
rs57155464611:69,950,114A/Guncertain significance
rs76828544911:69,954,481C/Tuncertain significance
rs57799191611:69,957,260C/Tlikely benign
rs37165241111:69,957,846C/Tuncertain significance
rs75501579811:69,962,576G/Auncertain significance
rs37464618511:69,970,464C/Tlikely benign
rs77042454311:69,970,468G/Cuncertain significance
rs77305510411:69,970,517T/Cuncertain significance
rs74782089811:69,972,175T/Cuncertain significance
rs159080428211:69,972,227G/Auncertain significance
rs55664424311:69,976,114G/A
rs77693615411:69,978,123G/Auncertain significance
rs36771675411:69,978,125G/Auncertain significance
rs55396969511:69,978,149G/Auncertain significance
rs249683574311:69,978,156T/Cuncertain significance
rs130071594811:69,978,167G/Auncertain significance
rs793991211:69,982,096G/Aintron variant
rs11722219811:69,988,348C/Tregulatory region variant
rs1227939711:69,995,059A/T
rs213562552111:69,995,830G/Tlikely pathogenic
rs20127243111:69,995,833C/Alikely benign
rs145992818111:69,995,867G/Auncertain significance
rs1079301711:70,000,459G/Tdownstream gene variant
rs56801017011:70,002,011C/Glikely benign
rs130642811411:70,002,020C/Tuncertain significance
rs204779699211:70,002,027A/Guncertain significance
rs11560014611:70,003,045T/Cbenign
rs76806554311:70,003,054C/Auncertain significance
rs1229583711:70,004,367G/C
rs87510711:70,005,374C/Aregulatory region variant
rs20000757111:70,007,273G/Auncertain significance
rs77359215611:70,007,294G/Auncertain significance
rs3428454411:70,007,335C/Tbenign
rs20187099011:70,007,354G/Alikely benign
rs77604693411:70,007,391C/Tuncertain significance
rs75729291611:70,007,439G/Auncertain significance
rs227606811:70,007,484C/Gintron variant
rs76897147811:70,007,740C/Tuncertain significance
rs3591616511:70,007,798T/Cbenign
rs37533546811:70,009,404G/Alikely benign
rs249723308711:70,011,597A/Gpathogenic
rs136298188411:70,013,376A/Cuncertain significance
rs20060655311:70,013,397C/Guncertain significance
rs20046317211:70,013,405C/Tlikely benign
rs76479141711:70,013,431G/Auncertain significance
rs14245733211:70,013,870G/Aintron variant
rs249730292411:70,017,014C/Tpathogenic
rs249730343011:70,017,038T/Cuncertain significance
rs37671936211:70,017,121G/Auncertain significance
rs204844924211:70,017,142A/Guncertain significance
rs36899489711:70,026,136A/Glikely benign
rs74694134211:70,028,740G/Auncertain significance
rs36768748411:70,028,753A/Guncertain significance
rs249746249711:70,028,756A/Tuncertain significance
rs52943318311:70,031,713A/Cuncertain significance
rs129256250211:70,031,725C/Tuncertain significance
rs249753707811:70,033,899A/Guncertain significance
rs20063685211:70,033,902A/Tuncertain significance
rs11445229911:70,033,945G/Cuncertain significance
rs75545531711:70,033,988A/Guncertain significance
rs20097090611:70,034,002G/Abenign
rs37557999311:70,034,018G/Auncertain significance
rs6173187011:70,034,065C/Tlikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.