ANO3

anoctamin 3

Summary

The protein encoded by this gene belongs to the TMEM16 family of predicted membrane proteins, that are also known as anoctamins. While little is known about the function of this gene, mutations in this gene have been associated with some cases of autosomal dominant craniocervical dystonia. Cells from individuals with a mutation in this gene exhibited abnormalities in endoplasmic reticulum-dependent calcium signaling. Studies in rat show that the rat ortholog of this protein interacts with, and modulates the activity of a sodium-activated potassium channel. Deletion of this gene caused increased pain sensitivity in the rat model system. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Aug 2015]

Known Variants435 total

rsidPosition (GRCh37)AllelesClassClinVar
rs136306737511:26,210,769T/Cuncertain significance
rs75949829711:26,210,827C/Glikely benign
rs14210839111:26,216,166G/T
rs7693849711:26,220,945C/Tregulatory region variant
rs7470785211:26,226,995A/Tintron variant
rs18971971111:26,341,858C/Tintron variant
rs1691548211:26,353,437C/Gbenign
rs153139511:26,353,561T/Cbenign
rs153139411:26,353,643T/Abenign
rs11405926911:26,353,680G/Alikely benign
rs14919578011:26,353,769C/Tlikely benign
rs1724325211:26,353,811T/Cbenign
rs75022080911:26,353,832C/Auncertain significance
rs95144382211:26,353,834T/Clikely benign
rs76276525911:26,353,839G/Tuncertain significance
rs249434625111:26,353,868G/Tuncertain significance
rs249434627011:26,353,871C/Tuncertain significance
rs1724325911:26,353,951T/Gbenign
rs19970506811:26,463,455G/Clikely benign
rs140878013111:26,463,465G/Tuncertain significance
rs37412034511:26,463,505G/Clikely benign
rs37338793111:26,463,518C/Guncertain significance
rs15099928211:26,463,539G/Auncertain significance
rs75929215611:26,463,540C/Tuncertain significance
rs91614298711:26,463,542C/Tuncertain significance
rs76717972011:26,463,546G/Auncertain significance
rs77506658011:26,463,550C/Tlikely benign
rs95026406811:26,463,573A/Guncertain significance
rs75084909311:26,463,578A/Guncertain significance
rs75878214111:26,463,579C/Tuncertain significance
rs6174629711:26,463,582C/Tconflicting classifications of pathogenicity
rs19279986211:26,463,598C/Tlikely benign
rs74814866911:26,463,599G/Auncertain significance
rs77093692211:26,463,600A/Clikely benign
rs13853401611:26,463,604T/Guncertain significance
rs105490602511:26,463,630C/Guncertain significance
rs213402395011:26,463,640C/Tlikely benign
rs249462006911:26,463,641A/Guncertain significance
rs37017884311:26,463,677T/Clikely benign
rs14027919111:26,465,310A/Clikely benign
rs249462504611:26,465,318C/Auncertain significance
rs94284009411:26,465,325G/Tuncertain significance
rs137843691511:26,465,327A/Guncertain significance
rs156502812911:26,465,333A/Guncertain significance
rs76838294011:26,465,335G/Auncertain significance
rs249462514711:26,465,340T/Clikely benign
rs19950339311:26,465,351G/Aconflicting classifications of pathogenicity
rs249462525911:26,465,360C/Tuncertain significance
rs88940254211:26,465,363A/Cuncertain significance
rs37040470111:26,465,365C/Aconflicting classifications of pathogenicity
rs11337379111:26,465,383G/Auncertain significance
rs403291811:26,465,500A/Gbenign
rs1730904811:26,484,301G/Alikely benign
rs794243211:26,484,496G/Cbenign
rs148123230011:26,484,573A/Glikely benign
rs76877312811:26,484,601C/Tuncertain significance
rs86839861311:26,484,603G/Cuncertain significance
rs13888907311:26,484,611A/Gbenign
rs77191623111:26,484,617C/Tlikely benign
rs100931077811:26,484,621A/Guncertain significance
rs37130867911:26,484,628A/Cuncertain significance
rs125452547811:26,484,631G/Auncertain significance
rs130867090211:26,484,633T/Cuncertain significance
rs99648303011:26,484,637G/Auncertain significance
rs14189202111:26,484,650C/Tlikely benign
rs75050122211:26,484,654G/Tuncertain significance
rs36865582111:26,484,661A/Gconflicting classifications of pathogenicity
rs19957442911:26,484,670C/Aconflicting classifications of pathogenicity
rs75361659211:26,484,680G/Alikely benign
rs76657570011:26,484,684A/Guncertain significance
rs77833859211:26,484,691C/Tuncertain significance
rs130192509911:26,484,699A/Guncertain significance
rs11396751111:26,484,860A/Glikely benign
rs18777932511:26,529,525C/Tlikely benign
rs249484894211:26,529,633T/Clikely benign
rs249484908811:26,529,647G/Tlikely benign
rs249484934811:26,529,682C/Tuncertain significance
rs122913140911:26,529,711G/Tuncertain significance
rs55901477311:26,529,741A/Gconflicting classifications of pathogenicity
rs20174435611:26,529,752T/Clikely benign
rs213413685211:26,529,764A/Glikely benign
rs37557048111:26,529,813G/Cuncertain significance
rs29402511:26,529,900G/Cbenign
rs11780627711:26,530,052G/Alikely benign
rs11797500011:26,530,079A/Glikely benign
rs11782421411:26,538,067C/Tbenign
rs7767795511:26,538,119G/Tbenign
rs249489660711:26,538,357C/Tlikely benign
rs53277509711:26,538,362T/Cbenign
rs77825303111:26,538,391C/Tlikely benign
rs131638982811:26,538,392G/Auncertain significance
rs37518074111:26,538,395A/Guncertain significance
rs186188374311:26,538,414A/Guncertain significance
rs74817180211:26,538,429C/Tuncertain significance
rs76959605911:26,538,430G/Alikely benign
rs148707294611:26,538,456A/Cuncertain significance
rs249489744111:26,538,475G/Auncertain significance
rs52728685011:26,538,622T/Clikely benign
rs11744014411:26,538,637C/Tbenign
rs11764519211:26,538,748G/Abenign

Showing 100 of 435 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.