AP5Z1

adaptor related protein complex 5 subunit zeta 1

Summary

This gene was identified by genome-wide screen for genes involved in homologous recombination DNA double-strand break repair (HR-DSBR). The encoded protein was found in a complex with other proteins that have a role in HR-DSBR. Knockdown of this gene reduced homologous recombination, and mutations in this gene were found in patients with spastic paraplegia. It was concluded that this gene likely encodes a helicase (PMID:20613862). [provided by RefSeq, Jan 2011]

Known Variants914 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1134038367:4,815,048G/Abenign
rs5313570457:4,815,067C/Alikely benign
rs1416806167:4,815,132G/Abenign
rs356848687:4,815,135A/Cbenign
rs1447129757:4,815,163T/Gbenign
rs5463546217:4,815,279G/Tuncertain significance
rs10490287347:4,815,321C/Tuncertain significance
rs1429836767:4,815,344G/Alikely benign
rs1461437237:4,815,346G/Clikely benign
rs2019716667:4,815,354C/Tuncertain significance
rs15832221637:4,815,368A/Cuncertain significance
rs3696879337:4,815,379C/Tlikely benign
rs12624335967:4,815,383G/Cuncertain significance
rs7664494297:4,815,392G/Tuncertain significance
rs7540148157:4,815,396G/Alikely benign
rs10378130317:4,815,402C/Tlikely benign
rs1399994617:4,815,403G/Abenign
rs7792414567:4,815,406C/Tlikely benign
rs37500157:4,815,528T/Gbenign
rs37500147:4,815,603T/Cbenign
rs736719207:4,815,619T/Glikely benign
rs1147420327:4,815,672C/Gbenign
rs171351157:4,820,581T/Cbenign
rs612159807:4,820,660C/Tlikely benign
rs559872807:4,820,662A/Tlikely benign
rs1431806247:4,820,729C/Tlikely benign
rs14699345617:4,820,806G/Auncertain significance
rs7653325967:4,820,813C/Tpathogenic
rs7529854367:4,820,818C/Tlikely benign
rs5484981067:4,820,819G/Auncertain significance
rs7520311107:4,820,821G/Tuncertain significance
rs7817433767:4,820,823A/Tuncertain significance
rs7453306997:4,820,826T/Guncertain significance
rs11981886527:4,820,831A/Tpathogenic
rs7683617387:4,820,844G/Auncertain significance
rs7479825847:4,820,847T/Auncertain significance
rs25340304647:4,820,862A/Guncertain significance
rs7522816857:4,820,871A/Guncertain significance
rs5276429937:4,820,881G/Aconflicting classifications of pathogenicity
rs3745929307:4,820,884C/Tlikely benign
rs1466823197:4,820,890C/Tconflicting classifications of pathogenicity
rs3708592687:4,820,891G/Auncertain significance
rs7708362867:4,820,914C/Tlikely benign
rs7747388747:4,820,922C/Apathogenic
rs1826947387:4,820,928C/Tuncertain significance
rs7508180397:4,820,935C/Tconflicting classifications of pathogenicity
rs7566310687:4,820,936A/Guncertain significance
rs2004232827:4,820,940G/Auncertain significance
rs11866998527:4,820,944G/Tlikely pathogenic
rs12552576767:4,820,946G/Auncertain significance
rs7490077467:4,820,958G/Alikely benign
rs1453990257:4,821,056T/Glikely benign
rs1144300217:4,821,171C/Tlikely benign
rs7723063487:4,821,180C/Tlikely benign
rs7610467627:4,821,183G/Alikely benign
rs5298875587:4,821,190G/Alikely benign
rs14815535577:4,821,196C/Tuncertain significance
rs3763351377:4,821,214C/Guncertain significance
rs3693407247:4,821,215G/Auncertain significance
rs7570477647:4,821,219A/Tuncertain significance
rs21151030407:4,821,228A/Tuncertain significance
rs7674173767:4,821,229G/Alikely benign
rs5604395477:4,821,238C/Tlikely benign
rs7482188847:4,821,239G/Auncertain significance
rs1995775597:4,821,257G/Auncertain significance
rs3690505347:4,821,277C/Tlikely benign
rs7758837527:4,821,278G/Aconflicting classifications of pathogenicity
rs7739795337:4,821,281G/Auncertain significance
rs7673253427:4,821,290C/Tlikely pathogenic
rs7502115077:4,821,291G/Auncertain significance
rs115498397:4,821,300C/Glikely benign
rs2018364827:4,821,302C/Tuncertain significance
rs5476061757:4,821,318G/Auncertain significance
rs17813868357:4,821,321T/Cuncertain significance
rs2004900937:4,821,332C/Tuncertain significance
rs5660017347:4,821,336C/Tuncertain significance
rs7692660097:4,821,337G/Alikely benign
rs13074634227:4,821,343C/Tlikely benign
rs7739744547:4,821,346C/Tlikely benign
rs7614469537:4,821,347C/Tuncertain significance
rs2014818027:4,821,348G/Auncertain significance
rs115498407:4,821,352G/Clikely benign
rs7604848947:4,821,362G/Cuncertain significance
rs7537305447:4,821,367C/Tlikely benign
rs3749121817:4,821,370C/Tconflicting classifications of pathogenicity
rs7652615907:4,821,371G/Auncertain significance
rs7516010757:4,821,374C/Guncertain significance
rs11816687767:4,821,380G/Auncertain significance
rs7506493787:4,821,381C/Tuncertain significance
rs7767909897:4,821,389G/Auncertain significance
rs1438000957:4,821,390C/Tconflicting classifications of pathogenicity
rs3746737557:4,821,394G/Alikely benign
rs3685585547:4,821,404C/Tlikely benign
rs768260757:4,821,555G/Abenign
rs1158097207:4,821,627C/Gbenign
rs1164945997:4,822,637C/Gbenign
rs1391352477:4,822,642C/Tbenign
rs797642707:4,822,778G/Cbenign
rs770869967:4,822,887T/Cbenign
rs15832300577:4,822,940T/Clikely benign

Showing 100 of 914 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.