ARV1

ARV1 fatty acid homeostasis modulator

Summary

this gene encodes a transmembrane protein that contains a conserved zinc ribbon motif at the N- terminus. A similar protein in mouse is thought to function in fatty acid homeostasis. Mutations in this gene are associated with early infantile epileptic encephalopathy 38. [provided by RefSeq, Nov 2016]

Known Variants42 total

rsidPosition (GRCh37)AllelesClassClinVar
rs111221741:231,114,595C/Tregulatory region variant
rs7744458291:231,114,853T/Clikely pathogenic
rs3680965561:231,114,860C/Tlikely benign
rs7478443451:231,114,880A/Guncertain significance
rs16787349021:231,114,900G/Auncertain significance
rs1435326931:231,114,915A/Tlikely benign
rs1402519591:231,114,924G/Tlikely benign
rs7521011661:231,114,932G/Tlikely benign
rs347457841:231,114,945T/Clikely benign
rs7785673401:231,114,952G/Auncertain significance
rs5781679431:231,114,976A/Guncertain significance
rs107798041:231,124,055T/Cbenign
rs7635988981:231,124,056A/Clikely benign
rs12943832611:231,124,064A/Glikely pathogenic
rs1418511041:231,124,070C/Auncertain significance
rs13039967081:231,124,105G/Auncertain significance
rs7495125041:231,124,108C/Tuncertain significance
rs1506193471:231,124,186G/Asplice region variantpathogenic
rs7461897541:231,125,851A/Guncertain significance
rs357648591:231,125,863G/Abenign
rs7777373761:231,125,915G/Cuncertain significance
rs7513445211:231,125,921A/Glikely benign
rs8680531351:231,126,010G/Tlikely pathogenic
rs16793441431:231,131,532T/Auncertain significance
rs3769375981:231,131,559A/Guncertain significance
rs356065651:231,131,585C/Tbenign
rs16793484091:231,131,602C/Tuncertain significance
rs7308822411:231,131,622G/Amissense variantpathogenic
rs1497042781:231,131,703C/Tuncertain significance
rs7679393271:231,131,712A/Cuncertain significance
rs1417828101:231,131,713A/Cuncertain significance
rs2019275591:231,131,724A/Guncertain significance
rs11926277431:231,132,865A/Tconflicting classifications of pathogenicity
rs5458411461:231,132,884C/Tuncertain significance
rs3681698671:231,132,885G/Auncertain significance
rs13477113661:231,132,905G/Alikely benign
rs7790806541:231,132,925G/Alikely benign
rs25276268191:231,132,939T/Auncertain significance
rs11892798241:231,132,952G/Cuncertain significance
rs7722560291:231,132,954G/Auncertain significance
rs2001141381:231,133,014G/Auncertain significance
rs5482149691:231,134,216A/G

Gene information from NCBI Gene. Variant classifications from ClinVar.