ASAH2

N-acylsphingosine amidohydrolase 2

Summary

Ceramidases (EC 3.5.1.23), such as ASAH2, catalyze hydrolysis of the N-acyl linkage of ceramide, a second messenger in a variety of cellular events, to produce sphingosine. Sphingosine exerts both mitogenic and apoptosis-inducing activities, and its phosphorylated form functions as an intra- and intercellular second messenger (see MIM 603730) (Mitsutake et al., 2001 [PubMed 11328816]).[supplied by OMIM, Mar 2008]

Known Variants21 total

rsidPosition (GRCh37)AllelesClassClinVar
rs75075346810:51,974,504C/Guncertain significance
rs78128174510:51,974,540G/Auncertain significance
rs104924093610:51,978,193A/G
rs76844510810:51,978,294C/Auncertain significance
rs117998094310:51,994,305T/Guncertain significance
rs20218381510:51,994,615C/G
rs123859383510:52,003,002C/Tuncertain significance
rs76659837310:52,003,017C/Tuncertain significance
rs7518508710:52,003,111T/Cuncertain significance
rs74934334510:52,005,004C/Auncertain significance
rs11604971910:52,005,095G/Astop gained
rs254064186710:52,005,106G/Auncertain significance
rs75778664210:52,005,121G/Auncertain significance
rs14171336910:52,005,146G/Auncertain significance
rs136986210:52,006,008A/C
rs127373030010:52,008,259T/Cuncertain significance
rs146622725410:52,008,272G/Cuncertain significance
rs18082233010:52,008,274T/Cuncertain significance
rs74561350710:52,008,307C/Tuncertain significance
rs1050892110:52,010,708C/Tupstream gene variant
rs1100480210:52,011,440G/Cupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.