ATOH8

atonal bHLH transcription factor 8

Summary

Enables DNA-binding transcription factor activity and E-box binding activity. Involved in several processes, including positive regulation of SMAD protein signal transduction; positive regulation of endothelial cell differentiation; and regulation of gene expression. Located in nucleoplasm. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants31 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7601492552:85,981,332T/Cuncertain significance
rs14001217192:85,981,415C/Guncertain significance
rs3696331182:85,981,458C/Guncertain significance
rs7759700092:85,981,501G/Tuncertain significance
rs13966288552:85,981,529C/Auncertain significance
rs7536158042:85,981,565C/Tuncertain significance
rs7787529972:85,981,574G/Auncertain significance
rs13196518432:85,981,575G/Tuncertain significance
rs7471237202:85,981,577G/Cuncertain significance
rs7461130172:85,981,592G/Alikely benign
rs7701222432:85,981,598C/Tuncertain significance
rs9104798442:85,981,613G/Auncertain significance
rs7714434672:85,981,619G/Cuncertain significance
rs12112422652:85,981,643T/Cuncertain significance
rs9593077362:85,981,650C/Tuncertain significance
rs13773262882:85,981,676C/Tuncertain significance
rs9779231152:85,981,685C/Tuncertain significance
rs10173401652:85,981,704C/Tuncertain significance
rs7811834192:85,981,734A/Cuncertain significance
rs3686936592:85,981,818C/Guncertain significance
rs7618916962:85,981,853C/Tuncertain significance
rs24668519712:85,982,034C/Auncertain significance
rs24668521032:85,982,063G/Cuncertain significance
rs5613166142:85,985,055C/T
rs1423448472:85,991,144T/Auncertain significance
rs1404263232:85,991,145C/Guncertain significance
rs7623084402:85,991,165A/Guncertain significance
rs2006366782:85,991,268G/Tuncertain significance
rs7777731002:85,991,301G/Auncertain significance
rs48320122:86,000,500G/A
rs359760242:86,003,971G/Aintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.