ATP6V1G1

ATPase H+ transporting V1 subunit G1

Summary

This gene encodes a component of vacuolar ATPase (V-ATPase), a multisubunit enzyme that mediates acidification of eukaryotic intracellular organelles. V-ATPase dependent organelle acidification is necessary for such intracellular processes as protein sorting, zymogen activation, receptor-mediated endocytosis, and synaptic vesicle proton gradient generation. V-ATPase is composed of a cytosolic V1 domain and a transmembrane V0 domain. The V1 domain consists of three A, three B, and two G subunits, as well as a C, D, E, F, and H subunit. The V1 domain contains the ATP catalytic site. The protein encoded by this gene is one of three V1 domain G subunit proteins. Pseudogenes of this gene have been characterized. [provided by RefSeq, Jul 2008]

Known Variants7 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7812319779:117,350,165A/Guncertain significance
rs18451399219:117,350,199A/Cuncertain significance
rs727525359:117,354,865A/Cmissense variant
rs1456277919:117,359,899A/Tuncertain significance
rs7464069109:117,359,902A/Cuncertain significance
rs5404253069:117,359,985C/Tuncertain significance
rs7545774979:117,360,009C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.