BAIAP2L1

BAR/IMD domain containing adaptor protein 2 like 1

Summary

This gene encodes a member of the IMD (IRSp53/MIM homology domain) family. Members of this family can be subdivided in two groups, the IRSp53-like and MIM-like, based on the presence or absence of the SH3 (Src homology 3) domain. The protein encoded by this gene contains a conserved IMD, also known as F-actin bundling domain, at the N-terminus, and a canonical SH3 domain near the C-terminus, so it belongs to the IRSp53-like group. This protein is the substrate for insulin receptor tyrosine kinase and binds to the small GTPase Rac. It is involved in signal transduction pathways that link deformation of the plasma membrane and remodeling of the actin cytoskeleton. It also promotes actin assembly and membrane protrusions when overexpressed in mammalian cells, and is essential to the formation of a potent actin assembly complex during EHEC (Enterohemorrhagic Escherichia coli) pedestal formation. [provided by RefSeq, Oct 2009]

Known Variants40 total

rsidPosition (GRCh37)AllelesClassClinVar
rs18000827547:97,923,404G/Auncertain significance
rs7633596397:97,933,557G/Auncertain significance
rs8961939887:97,933,566G/Auncertain significance
rs1467597137:97,933,580G/Tuncertain significance
rs1998467797:97,933,582C/Tuncertain significance
rs5392262077:97,933,583G/Alikely benign
rs7632649737:97,933,623G/Tuncertain significance
rs1389157077:97,933,648C/Tuncertain significance
rs7543045187:97,933,660C/Tuncertain significance
rs14218849687:97,935,766G/Tuncertain significance
rs7689907807:97,935,802G/Auncertain significance
rs12666831207:97,937,007G/Cuncertain significance
rs1472546517:97,937,012G/Tuncertain significance
rs3715216447:97,937,014C/Tuncertain significance
rs7784474627:97,937,096C/Auncertain significance
rs25350701947:97,937,166G/Auncertain significance
rs25350702817:97,937,178G/Auncertain significance
rs7603865107:97,939,856G/Auncertain significance
rs25350891527:97,941,461G/Auncertain significance
rs7594792687:97,941,473G/Tuncertain significance
rs9622620187:97,941,486C/Tuncertain significance
rs13519517847:97,941,502T/Guncertain significance
rs3699047397:97,941,545C/Tuncertain significance
rs1441399137:97,944,788T/Cuncertain significance
rs7605554117:97,944,830C/Guncertain significance
rs7566242117:97,944,896C/Guncertain significance
rs7488178307:97,944,902C/Tuncertain significance
rs3722616397:97,944,921C/Tuncertain significance
rs1401669287:97,946,565C/Tuncertain significance
rs3699195917:97,949,598A/Cuncertain significance
rs78075557:97,957,517G/Adownstream gene variant
rs16886067:97,974,851G/Aregulatory region variant
rs1469043087:97,984,389T/Auncertain significance
rs37791957:97,993,362T/Aintron variant
rs16356127:98,015,049G/T
rs64656817:98,016,246C/Tupstream gene variant
rs96492137:98,021,211A/Gintron variant
rs14819627707:98,030,138G/Cuncertain significance
rs7681067617:98,030,144C/Guncertain significance
rs624782367:98,030,377G/Aregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.