BBOF1

basal body orientation factor 1

Summary

Predicted to be involved in sperm axoneme assembly. Predicted to act upstream of or within several processes, including cilium movement involved in cell motility; negative regulation of microtubule depolymerization; and protein stabilization. Predicted to be located in axoneme; ciliary basal body; and sperm flagellum. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants22 total

rsidPosition (GRCh37)AllelesClassClinVar
rs87993111014:74,486,199G/Cuncertain significance
rs77300439314:74,486,213G/Auncertain significance
rs75970818014:74,486,231A/Tuncertain significance
rs75787236614:74,489,723G/Auncertain significance
rs250396469914:74,489,726A/Guncertain significance
rs6175256914:74,489,766G/Tuncertain significance
rs76884412314:74,489,785G/Cuncertain significance
rs20204794914:74,495,920A/Cuncertain significance
rs77914894014:74,495,923G/Auncertain significance
rs36820595514:74,497,636T/G
rs20091600214:74,497,638T/G
rs75635211114:74,512,767G/Auncertain significance
rs86700014014:74,512,798A/Guncertain significance
rs37109655614:74,512,820C/Tuncertain significance
rs139142353814:74,514,662T/Cuncertain significance
rs18588439814:74,514,758C/Auncertain significance
rs20008070814:74,516,434G/Tuncertain significance
rs206002448714:74,516,435A/Tuncertain significance
rs75552588314:74,516,564A/Guncertain significance
rs20142471814:74,516,856G/Cuncertain significance
rs14925949414:74,522,315G/Auncertain significance
rs37709076614:74,522,365A/Glikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.