CA1

carbonic anhydrase 1

Summary

Carbonic anhydrases (CAs) are a large family of zinc metalloenzymes that catalyze the reversible hydration of carbon dioxide. They participate in a variety of biological processes, including respiration, calcification, acid-base balance, bone resorption, and the formation of aqueous humor, cerebrospinal fluid, saliva and gastric acid. They show extensive diversity in tissue distribution and in their subcellular localization. This CA1 gene is closely linked to the CA2 and CA3 genes on chromosome 8. It encodes a cytosolic protein that is found at the highest level in erythrocytes. Allelic variants of this gene have been described in some populations. Alternative splicing and the use of alternative promoters results in multiple transcript variants. [provided by RefSeq, Nov 2016]

Known Variants32 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7667881868:86,240,805A/Guncertain significance
rs1219095778:86,240,815C/Gmissense variantpathogenic
rs1219095788:86,240,835C/Tmissense variantpathogenic
rs3713148918:86,240,856A/Guncertain significance
rs7546279398:86,240,881A/Tuncertain significance
rs7626562398:86,240,899G/Tuncertain significance
rs78274748:86,241,688G/Cintron variant
rs3771580378:86,241,942C/Guncertain significance
rs617344848:86,242,000G/Abenign
rs1425696268:86,242,037T/Cuncertain significance
rs617344858:86,244,732G/Abenign
rs78212488:86,245,776G/Abenign
rs1447461908:86,245,844G/Abenign
rs2021312238:86,249,176C/Tuncertain significance
rs15640234228:86,249,214C/Tuncertain significance
rs12571367848:86,249,221C/Tuncertain significance
rs7655118958:86,250,569A/Tuncertain significance
rs13662791248:86,250,627G/Cuncertain significance
rs7724856618:86,250,651G/Auncertain significance
rs7757607648:86,250,652G/Auncertain significance
rs1427149728:86,253,182G/Aintron variant
rs14965328:86,253,982C/Tintron variant
rs125443328:86,256,210C/Aintron variant
rs795693808:86,260,859C/Tintron variant
rs78414258:86,264,813C/A
rs1443627058:86,264,928C/Tintron variant
rs7256058:86,266,886C/G
rs15324238:86,268,313A/T
rs78247158:86,278,377C/Gintron variant
rs1131983198:86,279,697G/Tintron variant
rs132736548:86,286,557A/Gintron variant
rs1170725148:86,289,116C/Tintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.