CHST11

carbohydrate sulfotransferase 11

Summary

The protein encoded by this gene belongs to the sulfotransferase 2 family. It is localized to the golgi membrane, and catalyzes the transfer of sulfate to position 4 of the N-acetylgalactosamine (GalNAc) residue of chondroitin. Chondroitin sulfate constitutes the predominant proteoglycan present in cartilage, and is distributed on the surfaces of many cells and extracellular matrices. A chromosomal translocation involving this gene and IgH, t(12;14)(q23;q32), has been reported in a patient with B-cell chronic lymphocytic leukemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Aug 2011]

Known Variants33 total

rsidPosition (GRCh37)AllelesClassClinVar
rs20065371412:104,851,183C/Alikely benign
rs139774255712:104,851,193A/Cuncertain significance
rs127012645712:104,851,211G/Auncertain significance
rs126786444012:104,851,284A/Guncertain significance
rs1086122412:104,870,424G/Cintron variant
rs95844712:104,946,021G/A
rs57634862812:104,952,378G/A
rs7696094712:104,957,537T/Gintron variant
rs7922579712:104,976,498T/Cregulatory region variant
rs165013212:104,981,657A/Gupstream gene variant
rs5953997612:104,984,630G/C
rs75126553712:104,995,690G/Auncertain significance
rs14303462512:104,995,739C/Tlikely benign
rs1281169912:105,017,164C/Tintron variant
rs797806312:105,049,059G/C
rs83548712:105,060,767A/Gintron variant
rs83548812:105,061,008C/Tregulatory region variant
rs77159047812:105,087,971G/A
rs133159223912:105,150,727C/Tlikely benign
rs76755347912:105,150,767G/Auncertain significance
rs15046748812:105,150,812G/Auncertain significance
rs13832078512:105,150,818G/Alikely benign
rs77306098412:105,150,823G/Auncertain significance
rs75735876912:105,151,008G/Cuncertain significance
rs144434347912:105,151,040A/Guncertain significance
rs52762105512:105,151,046G/Auncertain significance
rs76337285512:105,151,090G/Auncertain significance
rs76324758412:105,151,177C/Tuncertain significance
rs131397247712:105,151,181A/Guncertain significance
rs14823056512:105,151,192G/Cconflicting classifications of pathogenicity
rs204048851312:105,151,219G/Auncertain significance
rs75829442012:105,151,234G/Auncertain significance
rs15077899012:105,151,387G/Alikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.