CPA5

carboxypeptidase A5

Summary

Carboxypeptidases have functions ranging from digestion of food to selective biosynthesis of neuroendocrine peptides. Members of the A/B subfamily of carboxypeptidases, such as CPA5, contain an approximately 90-amino acid pro region that assists in the folding of the active carboxypeptidase domain. Cleavage of the pro region activates the enzyme (Wei et al., 2002 [PubMed 11836249]).[supplied by OMIM, Mar 2008]

Known Variants40 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1436168877:129,983,414G/Aupstream gene variant
rs1997236707:129,986,352C/Guncertain significance
rs1910405117:129,986,381C/Guncertain significance
rs7824621337:129,986,421T/Glikely benign
rs1386571317:129,987,621G/Auncertain significance
rs1508942897:129,989,829G/Auncertain significance
rs1500290797:129,989,850T/Cuncertain significance
rs7820950777:129,989,867G/Auncertain significance
rs13057498767:129,989,934T/Cuncertain significance
rs731528537:129,995,129A/Gintron variant
rs798899567:129,996,938G/Aregulatory region variant
rs1436890377:129,999,473G/Auncertain significance
rs2005004177:129,999,482G/Auncertain significance
rs3687888847:130,001,030T/Cuncertain significance
rs2010490417:130,001,046T/Guncertain significance
rs7819911307:130,002,297C/Tuncertain significance
rs1998350237:130,002,298G/Alikely benign
rs1404654077:130,002,307C/Tuncertain significance
rs7827915867:130,002,339G/Auncertain significance
rs7820138647:130,002,789T/Cuncertain significance
rs1458236847:130,003,272C/Tuncertain significance
rs7825135717:130,003,311G/Auncertain significance
rs171648517:130,003,487G/T
rs7823621397:130,007,233C/Tuncertain significance
rs1479893327:130,007,251C/Guncertain significance
rs1420018707:130,007,270C/Tuncertain significance
rs8799468557:130,007,299T/Cuncertain significance
rs13421679117:130,007,333T/Cuncertain significance
rs7827256237:130,007,389C/Tuncertain significance
rs25359824487:130,007,751A/Guncertain significance
rs8689930077:130,007,775C/Tuncertain significance
rs7827559687:130,008,283T/Cuncertain significance
rs7826423017:130,008,305C/Auncertain significance
rs12786909807:130,008,323G/Auncertain significance
rs7819495657:130,008,354G/Alikely benign
rs7818598437:130,008,375G/Alikely benign
rs7822123837:130,008,395C/Tuncertain significance
rs3766435557:130,008,406A/Guncertain significance
rs102531137:130,009,311A/Gregulatory region variant
rs69755167:130,011,491C/A

Gene information from NCBI Gene. Variant classifications from ClinVar.