CRYAA

crystallin alpha A

Summary

Mammalian lens crystallins are divided into alpha, beta, and gamma families. Alpha crystallins are composed of two gene products: alpha-A and alpha-B, for acidic and basic, respectively. Alpha crystallins can be induced by heat shock and are members of the small heat shock protein (HSP20) family. They act as molecular chaperones although they do not renature proteins and release them in the fashion of a true chaperone; instead they hold them in large soluble aggregates. Post-translational modifications decrease the ability to chaperone. These heterogeneous aggregates consist of 30-40 subunits; the alpha-A and alpha-B subunits have a 3:1 ratio, respectively. Two additional functions of alpha crystallins are an autokinase activity and participation in the intracellular architecture. The encoded protein has been identified as a moonlighting protein based on its ability to perform mechanistically distinct functions. Alpha-A and alpha-B gene products are differentially expressed; alpha-A is preferentially restricted to the lens and alpha-B is expressed widely in many tissues and organs. Defects in this gene cause autosomal dominant congenital cataract (ADCC). [provided by RefSeq, Jan 2014]

Known Variants86 total

rsidPosition (GRCh37)AllelesClassClinVar
rs376138121:44,588,255C/Tupstream gene variant
rs1305310921:44,588,719G/Cupstream gene variant
rs727846821:44,588,757T/Gupstream gene variant
rs15110320221:44,589,148G/Alikely benign
rs198572923721:44,589,180C/Guncertain significance
rs87233121:44,589,215T/Cbenign
rs7431544021:44,589,236G/Astop gainedpathogenic
rs39751562421:44,589,243C/Tmissense variantpathogenic
rs77688481221:44,589,244G/Auncertain significance
rs14870406821:44,589,259T/Cuncertain significance
rs6172944221:44,589,263C/Tbenign
rs39751562521:44,589,270C/Tmissense variantpathogenic
rs39751562621:44,589,271G/Amissense variantpathogenic
rs75692604921:44,589,279G/Auncertain significance
rs75470144721:44,589,284G/Cuncertain significance
rs37363518721:44,589,290C/Tlikely benign
rs15121368721:44,589,320G/Alikely benign
rs76595257721:44,589,342A/Guncertain significance
rs86430968521:44,589,351T/Gmissense variantpathogenic
rs7431544121:44,589,354C/Tmissense variantpathogenic
rs75460770621:44,589,355G/Auncertain significance
rs14691478021:44,589,363C/Tconflicting classifications of pathogenicity
rs75829245921:44,589,368C/Tlikely benign
rs39751562321:44,589,369C/Tmissense variantpathogenic
rs77772881421:44,589,370G/Cconflicting classifications of pathogenicity
rs78111959321:44,589,375G/Auncertain significance
rs19151688921:44,589,412C/Tlikely benign
rs37722272121:44,589,413G/Alikely benign
rs5697519321:44,589,431C/Tlikely benign
rs7390646921:44,589,469G/Clikely benign
rs11733125321:44,589,522C/Tlikely benign
rs1170070921:44,589,569C/Tbenign
rs11682111521:44,590,366C/Tbenign
rs54413439621:44,590,477G/Alikely benign
rs76799110421:44,590,633T/Guncertain significance
rs52776569121:44,590,635C/Tlikely benign
rs74787262521:44,590,636G/Cuncertain significance
rs37616474421:44,590,639C/Tuncertain significance
rs6173585521:44,590,650C/Tbenign
rs75279061821:44,590,662C/Tlikely benign
rs20018364021:44,590,682C/Tuncertain significance
rs6173585621:44,590,683G/Abenign
rs37365207821:44,590,686G/Alikely benign
rs88605710321:44,590,706A/Cuncertain significance
rs75814647621:44,590,722G/Alikely benign
rs14472244221:44,590,728C/Tlikely benign
rs39812294721:44,590,729G/Amissense variantpathogenic
rs37185072521:44,590,740C/Tlikely benign
rs381916021:44,590,921A/Gbenign
rs7337621121:44,591,896G/Tlikely benign
rs7390647221:44,591,898G/Cbenign
rs7337621321:44,592,140G/Abenign
rs37424540521:44,592,183C/Tlikely benign
rs14551457421:44,592,189C/Tlikely benign
rs11380242621:44,592,192C/Tbenign
rs7910052921:44,592,195C/Tlikely benign
rs20059455521:44,592,203G/Auncertain significance
rs7431543921:44,592,214C/Tmissense variantpathogenic
rs12191297321:44,592,215G/Amissense variantpathogenic
rs76095878221:44,592,217C/Tuncertain significance
rs36960904621:44,592,223C/Tuncertain significance
rs76132457221:44,592,237C/Tuncertain significance
rs88605710421:44,592,243C/Auncertain significance
rs37700989421:44,592,248C/Tuncertain significance
rs251754917321:44,592,277G/Auncertain significance
rs6173585721:44,592,312T/Abenign
rs14399248421:44,592,332C/Auncertain significance
rs75758484321:44,592,349G/Auncertain significance
rs37649051121:44,592,354G/Alikely benign
rs88605710521:44,592,356G/Auncertain significance
rs132989925421:44,592,374C/Tuncertain significance
rs122705705121:44,592,376G/Auncertain significance
rs13979460921:44,592,382T/Cuncertain significance
rs11285537021:44,592,483G/Tbenign
rs56986628921:44,592,492T/Clikely benign
rs53738569821:44,592,493C/Tlikely benign
rs55305997521:44,592,546T/Guncertain significance
rs88605710621:44,592,583G/Auncertain significance
rs88605710721:44,592,643C/Tuncertain significance
rs88605710821:44,592,723G/Auncertain significance
rs88605710921:44,592,766G/Cuncertain significance
rs37001569721:44,592,770G/Auncertain significance
rs88605711021:44,592,788G/Auncertain significance
rs1304808921:44,592,875A/Gbenign
rs7961497021:44,592,897C/Gbenign
rs1191127521:44,593,140A/Gregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.

CRYAA — crystallin alpha A