CYP39A1

cytochrome P450 family 39 subfamily A member 1

Summary

This gene encodes a member of the cytochrome P450 superfamily of enzymes. The cytochrome P450 proteins are monooxygenases which catalyze many reactions involved in drug metabolism and synthesis of cholesterol, steroids and other lipids. This endoplasmic reticulum protein is involved in the conversion of cholesterol to bile acids. Its substrates include the oxysterols 25-hydroxycholesterol, 27-hydroxycholesterol and 24-hydroxycholesterol. Alternate splicing results in multiple transcript variants. [provided by RefSeq, Jul 2013]

Known Variants29 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7505602556:46,518,153C/Tuncertain significance
rs13917991286:46,518,155C/Tuncertain significance
rs122083606:46,521,249A/Tintron variant
rs5483484316:46,535,735A/T
rs25328056916:46,554,824A/Guncertain significance
rs77617316:46,563,817A/Tmissense variant
rs1415665576:46,588,112G/Aintron variant
rs25329791036:46,593,158C/Tuncertain significance
rs1379001586:46,593,166A/Guncertain significance
rs17752529476:46,593,170C/Guncertain significance
rs17752571036:46,593,211T/Auncertain significance
rs1493131456:46,593,222G/Alikely benign
rs17756212836:46,598,705C/Auncertain significance
rs5358991296:46,598,707G/Auncertain significance
rs15824401606:46,598,747T/Cuncertain significance
rs1478667246:46,604,145G/Clikely benign
rs3676725526:46,605,576A/Tuncertain significance
rs7557130166:46,605,663A/Glikely benign
rs15620150036:46,605,668A/Clikely benign
rs3680790756:46,605,681A/Cuncertain significance
rs5528626396:46,605,684G/Cuncertain significance
rs5323337776:46,605,687T/Cuncertain significance
rs1408541976:46,607,391T/Cuncertain significance
rs6662406:46,607,708C/Tintron variant
rs5406127546:46,609,912C/Auncertain significance
rs7804932996:46,610,014A/Guncertain significance
rs7764653456:46,620,191A/Cuncertain significance
rs616618286:46,620,240C/Tlikely benign
rs12639244996:46,620,241G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.