CYP3A4

cytochrome P450 family 3 subfamily A member 4

Pharmacogene

Summary

This gene encodes a member of the cytochrome P450 superfamily of enzymes. The cytochrome P450 proteins are monooxygenases that catalyze many reactions involved in drug metabolism and synthesis of cholesterol, steroids and other lipids. This protein localizes to the endoplasmic reticulum and its expression is induced by glucocorticoids and some pharmacological agents. This enzyme is involved in the metabolism of approximately half the drugs in use today, including acetaminophen, codeine, cyclosporin A, diazepam, erythromycin, and chloroquine. The enzyme also metabolizes some steroids and carcinogens. This gene is part of a cluster of cytochrome P450 genes on chromosome 7q21.1. Previously another CYP3A gene, CYP3A3, was thought to exist; however, it is now thought that this sequence represents a transcript variant of CYP3A4. Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Aug 2020]

Known Variants49 total

rsidPosition (GRCh37)AllelesClassClinVar
rs355993677:99,354,604C/Tintronic
rs7655989207:99,355,805G/Tuncertain significance
rs37354517:99,355,975T/Cintron variant
rs49869137:99,358,459G/Amissense variant
rs49869107:99,358,524A/Gmissense variant
rs24858672527:99,358,531T/Cuncertain significance
rs10419887:99,358,566A/Gmissense variant
rs357235177:99,359,655G/Abenign
rs49869097:99,359,670G/Cmissense variant
rs21515544337:99,359,763C/Tuncertain significance
rs127216297:99,359,800G/Amissense variant
rs677843557:99,359,829G/Amissense variantlikely benign
rs12704540097:99,359,877T/Cuncertain significance
rs46464407:99,360,870G/Aregulatory region variant
rs22424807:99,361,466C/Tupstream gene variantdrug response
rs18154136557:99,361,602A/Gpathogenic
rs283717597:99,361,626A/Gmissense variantuncertain significance
rs355642777:99,362,436T/Cupstream gene variant
rs32083637:99,364,798A/Tmissense variant
rs46464377:99,365,083G/Adownstream gene variantdrug response
rs22467097:99,365,719A/Gdownstream gene variant
rs26871167:99,365,943C/T
rs557853407:99,365,983A/Gmissense variant
rs559012637:99,365,994G/Cmissense variant
rs14182579107:99,366,033T/Cuncertain significance
rs49871597:99,366,068G/Abenign
rs32083617:99,366,070T/Cmissense variant
rs9067833967:99,366,071G/Cuncertain significance
rs49871617:99,366,081A/Gmissense variant
rs127216277:99,366,093G/Cmissense variant
rs49869087:99,367,392C/Gmissense variant
rs49869077:99,367,427C/Tmissense variant
rs725527997:99,367,788C/Tmissense variant
rs18155922397:99,367,802T/Auncertain significance
rs559516587:99,367,825T/Cmissense variant
rs30913397:99,370,245T/Cmissense variant
rs563241287:99,375,702C/Tmissense variant
rs24859091127:99,377,707A/Guncertain significance
rs127216347:99,381,661A/Gmissense variant
rs27405747:99,382,096A/Gregulatorybenign
rs117735977:99,382,451G/Cupstream gene variant
rs676668217:99,758,183G/GTframeshift variant
rs2018217087:99,763,925T/Cmissense variant
rs7660606027:99,763,949C/Tmissense variant
rs46464387:99,766,411G/GTframeshift variant
rs1381056387:99,766,440G/Astop gained
rs1136673577:99,768,424T/Amissense variantlikely benign
rs725527987:99,769,781C/Tmissense variant
rs574096227:99,769,805G/Amissense variant

Gene information from NCBI Gene. Variant classifications from ClinVar.