CYP3A5

cytochrome P450 family 3 subfamily A member 5

Pharmacogene

Summary

This gene encodes a member of the cytochrome P450 superfamily of enzymes. The cytochrome P450 proteins are monooxygenases which catalyze many reactions involved in drug metabolism and synthesis of cholesterol, steroids and other lipids. The encoded protein metabolizes drugs as well as the steroid hormones testosterone and progesterone. This gene is part of a cluster of cytochrome P450 genes on chromosome 7q21.1. Two pseudogenes of this gene have been identified within this cluster on chromosome 7. Expression of this gene is widely variable among populations, and a single nucleotide polymorphism that affects transcript splicing has been associated with susceptibility to hypertensions. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Apr 2014]

Known Variants51 total

rsidPosition (GRCh37)AllelesClassClinVar
rs155247:99,245,914A/G3 prime UTR variant
rs283650857:99,245,974A/Gmissense variant
rs5598635377:99,246,004G/Auncertain significance
rs283650697:99,246,026A/Gbenign
rs14501165797:99,247,712G/Tuncertain significance
rs412798547:99,247,772A/Gmissense variant
rs18090286647:99,247,778A/Guncertain significance
rs10567256687:99,250,186G/Auncertain significance
rs15844067447:99,250,223G/Alikely benign
rs283650837:99,250,236G/Tmissense variant
rs2006282087:99,250,238T/Glikely benign
rs7518322067:99,250,255A/Guncertain significance
rs7651080017:99,250,264G/Anot provided
rs18093073937:99,250,287A/Guncertain significance
rs13633201867:99,250,389T/Cuncertain significance
rs762933807:99,250,394
rs11966726487:99,250,398G/Tuncertain significance
rs123340727:99,251,707A/T
rs77803287:99,256,844A/C
rs1878869677:99,257,503C/Tintron variant
rs283834797:99,258,139C/Tmissense variant
rs7730302127:99,258,142C/Auncertain significance
rs7666950067:99,258,222G/Tuncertain significance
rs7555968387:99,258,253A/Cuncertain significance
rs46464537:99,260,362C/Aintron variant
rs7542371337:99,260,632C/Tlikely benign
rs3767734327:99,261,610C/Tuncertain significance
rs24853852707:99,261,624T/Alikely benign
rs413033437:99,262,835T/insframeshift
rs564114027:99,262,860T/Cmissense variant
rs24854066997:99,262,884T/Cuncertain significance
rs1399515977:99,264,240G/Auncertain significance
rs7521107607:99,264,291A/Guncertain significance
rs559654227:99,264,573A/Gsplice region variant
rs1998662237:99,264,648A/Guncertain significance
rs412798577:99,270,222G/Tmissense variantlikely benign
rs7590991837:99,270,244C/Auncertain significance
rs562444477:99,270,276A/Cmissense variant
rs18118150217:99,270,537T/Cuncertain significance
rs7767467:99,270,539A/Gsplice variantrisk factor
rs102642727:99,270,868C/Tsplice variantlikely benign
rs725527917:99,273,745T/Cmissense variant
rs12412445047:99,273,746A/Guncertain significance
rs1509999437:99,273,765C/Alikely benign
rs283834687:99,273,815G/Amissense variantlikely benign
rs558179507:99,273,821G/Amissense variant
rs1152679787:99,273,942G/Abenign
rs1119603617:99,273,983A/Glikely benign
rs3691708737:99,277,497G/Auncertain significance
rs283717647:99,277,593G/Alikely benign
rs283650957:99,277,605C/Tlikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.