DDX27

DEAD-box helicase 27

Summary

DEAD box proteins, characterized by the conserved motif Asp-Glu-Ala-Asp (DEAD), are putative RNA helicases. They are implicated in a number of cellular processes involving alteration of RNA secondary structure such as translation initiation, nuclear and mitochondrial splicing, and ribosome and spliceosome assembly. Based on their distribution patterns, some members of this family are believed to be involved in embryogenesis, spermatogenesis, and cellular growth and division. This gene encodes a DEAD box protein involved in the processing of 5.8S and 28S ribosomal RNAs. More specifically, the encoded protein localizes to the nucleolus, where it interacts with the PeBoW complex to ensure proper 3' end formation of 47S rRNA. [provided by RefSeq, Jan 2017]

Known Variants42 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14601103920:47,835,942G/Tuncertain significance
rs14166173420:47,835,953G/Auncertain significance
rs75025902320:47,835,998C/Tuncertain significance
rs20030429920:47,836,006A/Clikely benign
rs251673038320:47,836,035T/Auncertain significance
rs77676025620:47,837,995A/Guncertain significance
rs53232326120:47,839,891G/Tuncertain significance
rs74789707820:47,839,935A/Guncertain significance
rs76987763720:47,839,943G/Auncertain significance
rs11743888720:47,839,969A/Gbenign
rs612559720:47,840,772T/Cintron variant
rs37770622120:47,841,506A/Guncertain significance
rs15123939720:47,841,650G/Abenign
rs6174837720:47,841,706G/Alikely benign
rs1190834720:47,842,015C/Tintron variant
rs128001473020:47,842,997A/Guncertain significance
rs1190749720:47,843,620T/Cintron variant
rs23816620:47,845,262C/Tbenign
rs14474885520:47,845,311G/Auncertain significance
rs76050599220:47,845,323C/Tuncertain significance
rs13867394620:47,845,345C/Tuncertain significance
rs37482187820:47,846,778C/Tuncertain significance
rs77259537520:47,846,785C/Guncertain significance
rs1303886620:47,849,216G/Aintron variant
rs74921520320:47,849,905G/Auncertain significance
rs87343420:47,851,624C/Tuncertain significance
rs130948481920:47,852,718G/Auncertain significance
rs95707450620:47,852,758G/Auncertain significance
rs37436576720:47,852,767C/Tuncertain significance
rs14106718220:47,852,981C/Tuncertain significance
rs78077882420:47,852,998G/Tuncertain significance
rs251675244620:47,853,018C/Tuncertain significance
rs74896102420:47,853,042C/Tuncertain significance
rs77245351120:47,855,503C/Tuncertain significance
rs74866613120:47,855,777A/Cuncertain significance
rs20129051520:47,855,830G/Auncertain significance
rs3575903020:47,858,290G/Abenign
rs198048700420:47,858,438G/Auncertain significance
rs77480499320:47,858,740C/Tuncertain significance
rs77302872820:47,859,175C/Tuncertain significance
rs91343477320:47,860,189A/Cuncertain significance
rs14151387420:47,860,212C/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.