DECR1

2,4-dienoyl-CoA reductase 1

Summary

Enables 2,4-dienoyl-CoA reductase (NADPH) activity; NADPH binding activity; and identical protein binding activity. Involved in fatty acid beta-oxidation. Located in cytosol; mitochondrion; and nucleoplasm. Part of catalytic complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants30 total

rsidPosition (GRCh37)AllelesClassClinVar
rs10095930278:91,013,739G/Tuncertain significance
rs7816135008:91,013,773G/Tuncertain significance
rs10202726638:91,013,778G/Auncertain significance
rs18058078:91,019,047C/Tupstream gene variant
rs343948398:91,019,051G/Aupstream gene variant
rs1453233358:91,029,359G/Alikely benign
rs1450665228:91,029,456A/Gsynonymous variant
rs14513241448:91,029,484G/Auncertain significance
rs1499014868:91,029,540C/Tlikely benign
rs7679105678:91,031,145A/Guncertain significance
rs1387258048:91,031,349T/Cbenign
rs1920127188:91,031,351T/Cuncertain significance
rs13175636368:91,031,352G/Auncertain significance
rs7749000358:91,031,353G/Auncertain significance
rs7599245428:91,033,137A/Glikely benign
rs1379042448:91,033,151T/Cbenign
rs12722149408:91,033,170T/Cuncertain significance
rs3726301278:91,033,242G/Alikely benign
rs7745516438:91,049,122G/Tuncertain significance
rs1890452598:91,051,553G/Aintron variant
rs5334504588:91,055,009C/Tlikely benign
rs1447884968:91,057,090G/Auncertain significance
rs7594625028:91,057,129G/Alikely benign
rs7785996798:91,057,170G/Auncertain significance
rs1485499548:91,057,198A/Glikely benign
rs15861656618:91,057,217T/Clikely benign
rs18140972518:91,063,905G/Auncertain significance
rs7792043388:91,063,920G/Auncertain significance
rs24885030808:91,063,921G/Auncertain significance
rs2001228468:91,064,118G/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.