DPP3

dipeptidyl peptidase 3

Summary

This gene encodes a protein that is a member of the M49 family of metallopeptidases. This cytoplasmic protein binds a single zinc ion with its zinc-binding motif (HELLGH) and has post-proline dipeptidyl aminopeptidase activity, cleaving Xaa-Pro dipeptides from the N-termini of proteins. Increased activity of this protein is associated with endometrial and ovarian cancers. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Feb 2012]

Known Variants59 total

rsidPosition (GRCh37)AllelesClassClinVar
rs227986411:66,247,844G/Aregulatory region variant
rs74798718511:66,249,690A/Cuncertain significance
rs20077781611:66,249,700A/Guncertain significance
rs14968939011:66,249,705A/Guncertain significance
rs90020185211:66,249,718G/Auncertain significance
rs13901833011:66,249,730G/Auncertain significance
rs14247805011:66,249,736C/Guncertain significance
rs20165847311:66,249,741C/Tuncertain significance
rs55769744211:66,249,787G/Auncertain significance
rs124701119611:66,249,838C/Tuncertain significance
rs53691837211:66,249,888G/Auncertain significance
rs1182668311:66,249,898G/Abenign
rs20163633111:66,249,927G/Auncertain significance
rs18708247711:66,252,639C/Gbenign
rs92915598511:66,252,645C/Tuncertain significance
rs249564258411:66,252,696C/Auncertain significance
rs14122740711:66,254,092G/Auncertain significance
rs77907432211:66,254,128C/Tuncertain significance
rs11248460611:66,254,137C/Abenign
rs11321622011:66,254,157C/Gbenign
rs155504147611:66,254,814G/Auncertain significance
rs74668057511:66,255,424G/Auncertain significance
rs78088799411:66,258,732C/Guncertain significance
rs77945138311:66,258,774C/Tuncertain significance
rs76233551111:66,258,798C/Tuncertain significance
rs20083443811:66,258,810G/Auncertain significance
rs14913608111:66,258,813C/Tuncertain significance
rs14225219311:66,258,814C/Tuncertain significance
rs76481238411:66,259,005A/Guncertain significance
rs36894130511:66,259,037G/Auncertain significance
rs185539097711:66,259,075C/Auncertain significance
rs1784948011:66,260,191C/Tbenign
rs20047359111:66,260,192G/Auncertain significance
rs20051762611:66,260,232G/Auncertain significance
rs20067427111:66,260,242G/Alikely benign
rs20012660011:66,260,342G/Cuncertain significance
rs14751914911:66,260,557G/Abenign
rs249566864611:66,260,582G/Auncertain significance
rs77536142411:66,260,615C/Tuncertain significance
rs14793225111:66,260,623G/Abenign
rs7677767511:66,261,044C/Tbenign
rs20155475911:66,261,099G/Auncertain significance
rs14732860211:66,262,711C/Tuncertain significance
rs3450406911:66,262,944C/Tconflicting classifications of pathogenicity
rs76065623711:66,263,112T/Cuncertain significance
rs134629620911:66,263,135G/Auncertain significance
rs20041738811:66,263,166G/Auncertain significance
rs20204074811:66,264,781G/Tuncertain significance
rs14161335011:66,264,859G/Auncertain significance
rs20216332311:66,264,865C/Tuncertain significance
rs129772347211:66,264,922C/Guncertain significance
rs11440724911:66,272,128G/Abenign
rs74673045311:66,272,153C/Tuncertain significance
rs15083149511:66,272,158C/Tuncertain significance
rs20024308111:66,272,197C/Tuncertain significance
rs13925103611:66,272,198G/Cuncertain significance
rs77350937211:66,273,953T/G
rs6156111111:66,275,923T/Cupstream gene variant
rs20184808011:66,276,636G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.