DPYSL2

dihydropyrimidinase like 2

Summary

This gene encodes a member of the collapsin response mediator protein family. Collapsin response mediator proteins form homo- and hetero-tetramers and facilitate neuron guidance, growth and polarity. The encoded protein promotes microtubule assembly and is required for Sema3A-mediated growth cone collapse, and also plays a role in synaptic signaling through interactions with calcium channels. This gene has been implicated in multiple neurological disorders, and hyperphosphorylation of the encoded protein may play a key role in the development of Alzheimer's disease. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Sep 2011]

Known Variants41 total

rsidPosition (GRCh37)AllelesClassClinVar
rs48724498:26,370,514G/Aregulatory region variant
rs14428858:26,395,258C/Aintron variant
rs4186248:26,431,560T/G
rs1383408078:26,439,487C/Amissense variantpathogenic
rs12123388968:26,439,534C/Tuncertain significance
rs7470634578:26,441,375G/Alikely benign
rs7534749568:26,441,459A/Glikely benign
rs22289798:26,481,697G/Abenign
rs9649242268:26,481,727G/Auncertain significance
rs1995077298:26,481,806C/Tuncertain significance
rs1391232178:26,481,822C/Tlikely benign
rs1116861788:26,484,172G/Alikely benign
rs25359914548:26,484,761A/Guncertain significance
rs7733357678:26,484,796C/Tlikely benign
rs7629976828:26,484,797G/Auncertain significance
rs7710706788:26,485,446G/Auncertain significance
rs119952278:26,486,255C/Tregulatory region variant
rs78325768:26,486,742A/Gintron variant
rs12735384858:26,492,302G/Auncertain significance
rs356213238:26,492,331C/Tbenign
rs3736624658:26,492,336A/Guncertain significance
rs1998691018:26,500,997C/Tuncertain significance
rs2008463588:26,500,998G/Clikely benign
rs3724084158:26,501,018G/Auncertain significance
rs3750959848:26,501,050A/Guncertain significance
rs1441322418:26,501,492C/Guncertain significance
rs1132137048:26,501,493C/Gbenign
rs14266417388:26,501,501C/Tuncertain significance
rs7692186728:26,501,524G/Auncertain significance
rs25360104508:26,501,552C/Tuncertain significance
rs7486091958:26,505,275C/Tuncertain significance
rs9151867178:26,505,278G/Auncertain significance
rs1510508918:26,505,283C/Tbenign
rs1391631628:26,505,307A/Clikely benign
rs5482497088:26,509,788A/Glikely benign
rs7791342788:26,509,809C/Tuncertain significance
rs25360193708:26,509,901C/Glikely benign
rs1454837028:26,510,739G/Abenign
rs25360207488:26,510,756G/Tuncertain significance
rs18033181148:26,510,866A/Guncertain significance
rs7544737388:26,513,168C/Gbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.