EDA2R

ectodysplasin A2 receptor

Summary

The protein encoded by this gene is a type III transmembrane protein of the TNFR (tumor necrosis factor receptor) superfamily, and contains cysteine-rich repeats and a single transmembrane domain. This protein binds to the EDA-A2 isoform of ectodysplasin, which plays an important role in maintenance of hair and teeth. Alternatively spliced transcript variants encodes distinct protein isoforms. [provided by RefSeq, Apr 2016]

Known Variants28 total

rsidPosition (GRCh37)AllelesClassClinVar
rs756693141X:65,817,849T/Alikely benign
rs921680648X:65,819,396C/Tuncertain significance
rs201070562X:65,819,397C/Aconflicting classifications of pathogenicity
rs2519554886X:65,819,492C/Tuncertain significance
rs150986690X:65,819,494C/Tbenign
rs766654958X:65,819,507G/Tuncertain significance
rs1928171564X:65,819,535G/Auncertain significance
rs749216567X:65,819,560G/Alikely benign
rs760870811X:65,819,580G/Auncertain significance
rs777625658X:65,819,615G/Auncertain significance
rs766939798X:65,819,618T/Cuncertain significance
rs778940212X:65,819,646C/Tlikely benign
rs2519632201X:65,822,514G/Auncertain significance
rs146403451X:65,822,614C/Tlikely benign
rs12837393X:65,824,281G/Alikely benign
rs769441083X:65,824,286T/Guncertain significance
rs755280381X:65,824,332G/Auncertain significance
rs200268345X:65,824,340C/Tlikely benign
rs1929413423X:65,824,924T/Guncertain significance
rs1385699X:65,824,986C/Tmissense variant
rs752010334X:65,825,021A/Tlikely benign
rs757586946X:65,825,022G/Auncertain significance
rs147641504X:65,835,784G/Abenign
rs759036337X:65,835,804C/Tlikely benign
rs769890219X:65,835,819C/Tuncertain significance
rs73221529X:65,835,841A/Gbenign
rs12850857X:65,852,279C/A
rs73221531X:65,853,557C/Tregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.