FBXL2

F-box and leucine rich repeat protein 2

Summary

This gene encodes a member of the F-box protein family which is characterized by an approximately 40 amino acid motif, the F-box. The F-box proteins constitute one of the four subunits of ubiquitin protein ligase complex called SCFs (SKP1-cullin-F-box), which function in phosphorylation-dependent ubiquitination. The F-box proteins are divided into 3 classes: Fbws containing WD-40 domains, Fbls containing leucine-rich repeats, and Fbxs containing either different protein-protein interaction modules or no recognizable motifs. The protein encoded by this gene belongs to the Fbls class and, in addition to an F-box, contains 12 tandem leucine-rich repeats. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jan 2010]

Known Variants12 total

rsidPosition (GRCh37)AllelesClassClinVar
rs5333490323:33,317,168T/G
rs1129864173:33,357,981T/Cintron variant
rs3732634003:33,400,815G/Tuncertain significance
rs7479500973:33,406,121G/Auncertain significance
rs1464479863:33,408,869C/Tintron variant
rs20424019783:33,414,634G/Auncertain significance
rs24706591593:33,414,797G/Clikely benign
rs9461818833:33,418,782G/Auncertain significance
rs22918973:33,419,422C/Tregulatory region variant
rs11930017543:33,420,189A/Cuncertain significance
rs7668493963:33,425,549T/Guncertain significance
rs7655293293:33,427,035G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.