FBXO28

F-box protein 28

Summary

Members of the F-box protein family, such as FBXO28, are characterized by an approximately 40-amino acid F-box motif. SCF complexes, formed by SKP1 (MIM 601434), cullin (see CUL1; MIM 603134), and F-box proteins, act as protein-ubiquitin ligases. F-box proteins interact with SKP1 through the F box, and they interact with ubiquitination targets through other protein interaction domains (Jin et al., 2004 [PubMed 15520277]).[supplied by OMIM, Mar 2008]

Known Variants34 total

rsidPosition (GRCh37)AllelesClassClinVar
rs2010436431:224,301,831G/Clikely benign
rs16565822791:224,301,845C/Guncertain significance
rs13521147601:224,301,851A/Tuncertain significance
rs1438315811:224,301,853C/Alikely benign
rs9354476561:224,301,875G/Cuncertain significance
rs14275696861:224,301,893G/Auncertain significance
rs7718162731:224,301,917C/Guncertain significance
rs21026045131:224,301,928C/Tuncertain significance
rs21026046341:224,302,022T/Gpathogenic
rs25271058141:224,302,082T/Cuncertain significance
rs7724335591:224,302,089G/Cuncertain significance
rs20489971:224,305,486G/C
rs107994781:224,305,966A/Tintron variant
rs13367041231:224,321,796A/Guncertain significance
rs25271502021:224,321,918A/Tuncertain significance
rs1457114191:224,339,832T/Cintron variant
rs1397259151:224,340,863G/Auncertain significance
rs25271973791:224,340,880A/Guncertain significance
rs1996727781:224,340,881A/Guncertain significance
rs25271974191:224,340,896C/Tuncertain significance
rs13341123691:224,340,970A/Guncertain significance
rs21026350971:224,341,030T/Cuncertain significance
rs14719112741:224,341,031C/Guncertain significance
rs1494421371:224,341,036C/Tlikely benign
rs75209561:224,341,924T/C
rs1892501471:224,345,067T/Clikely benign
rs10234719901:224,345,173C/Auncertain significance
rs7612948371:224,345,180G/Auncertain significance
rs2013639161:224,345,351G/Auncertain significance
rs25272096531:224,345,374C/Tuncertain significance
rs21026385901:224,345,383C/Gpathogenic
rs15532929871:224,345,384G/Tlikely pathogenic
rs1433819461:224,345,397G/Clikely benign
rs21026386311:224,345,419A/Tpathogenic

Gene information from NCBI Gene. Variant classifications from ClinVar.