FCN3

ficolin 3

Summary

Ficolins are a group of proteins which consist of a collagen-like domain and a fibrinogen-like domain. In human serum, there are two types of ficolins, both of which have lectin activity. The protein encoded by this gene is a thermolabile beta-2-macroglycoprotein found in all human serum and is a member of the ficolin/opsonin p35 lectin family. The protein, which was initially identified based on its reactivity with sera from patients with systemic lupus erythematosus, has been shown to have a calcium-independent lectin activity. The protein can activate the complement pathway in association with MASPs and sMAP, thereby aiding in host defense through the activation of the lectin pathway. Alternative splicing occurs at this locus and two variants, each encoding a distinct isoform, have been identified. [provided by RefSeq, Jul 2008]

Known Variants35 total

rsidPosition (GRCh37)AllelesClassClinVar
rs2022306641:27,695,744G/Auncertain significance
rs7482786771:27,695,773C/Tuncertain significance
rs7466748951:27,695,830C/Tuncertain significance
rs1432444881:27,695,848C/Guncertain significance
rs15575743651:27,695,863T/Cuncertain significance
rs283856521:27,695,877G/Alikely benign
rs7745685911:27,695,968C/Guncertain significance
rs44941571:27,696,837G/Trisk factor
rs1497347121:27,697,096C/Guncertain significance
rs7810530781:27,697,125T/Cuncertain significance
rs5464492471:27,697,149C/Tuncertain significance
rs7643519431:27,697,150G/Auncertain significance
rs25224194351:27,697,180T/Cuncertain significance
rs7458142861:27,697,206C/Tuncertain significance
rs1885666591:27,697,345A/Guncertain significance
rs564050861:27,697,359C/Glikely benign
rs12044347581:27,697,399C/Tuncertain significance
rs1996894971:27,697,417C/Auncertain significance
rs3734430591:27,697,424G/Auncertain significance
rs5541409531:27,697,441C/Tuncertain significance
rs38138001:27,697,474G/Tupstream gene variant
rs728827501:27,698,730A/Cintron variant
rs107945011:27,699,449A/Tregulatory region variantuncertain significance
rs1482345401:27,699,626C/Tuncertain significance
rs7616151291:27,699,634C/Tuncertain significance
rs7695056391:27,699,635C/Tuncertain significance
rs12933876151:27,699,715G/Tuncertain significance
rs1423972001:27,699,753G/Alikely benign
rs283857231:27,699,761A/Glikely benign
rs1405907441:27,699,990C/Tuncertain significance
rs13625583411:27,700,011C/Guncertain significance
rs1413001991:27,700,455C/Tuncertain significance
rs13543647531:27,700,479T/Cuncertain significance
rs7463002701:27,700,892C/Tuncertain significance
rs1471420561:27,701,301T/Clikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.