FMO4

flavin containing dimethylaniline monoxygenase 4

Summary

Metabolic N-oxidation of diet-derived amino-trimethylamine (TMA) is mediated by flavin-containing monooxygenase and is subject to an inherited FMO3 polymorphism in man. This results in a small subpopulation with reduced TMA N-oxidation capacity and causes fish odor syndrome (Trimethylaminuria). Three forms of the enzyme are encoded by genes clustered in the 1q23-q25 region. Flavin-containing monooxygenases are NADPH-dependent flavoenzymes that catalyzes the oxidation of soft nucleophilic heteroatom centers in drugs, pesticides, and xenobiotics. [provided by RefSeq, Jan 2015]

Known Variants37 total

rsidPosition (GRCh37)AllelesClassClinVar
rs609064811:171,289,025T/Cuncertain significance
rs14731332321:171,289,033T/Guncertain significance
rs8663743891:171,289,047C/Auncertain significance
rs1507525221:171,289,076G/Cuncertain significance
rs25259715841:171,292,198G/Tuncertain significance
rs11834297071:171,292,254A/Tuncertain significance
rs25259728571:171,292,324A/Tuncertain significance
rs7469844141:171,293,278C/Tuncertain significance
rs7813423991:171,293,288C/Guncertain significance
rs7701176181:171,293,296C/Tuncertain significance
rs3681447281:171,293,320C/Tuncertain significance
rs7672447511:171,300,850C/Tuncertain significance
rs2008091291:171,300,853G/Alikely benign
rs1382594471:171,300,908G/Auncertain significance
rs617475011:171,301,882T/Alikely benign
rs3769081071:171,301,885G/Cuncertain significance
rs25260243641:171,301,894C/Tuncertain significance
rs12688719011:171,302,040A/Tuncertain significance
rs10110722101:171,303,563T/Cuncertain significance
rs37379261:171,303,565C/Tbenign
rs7697369891:171,303,575G/Auncertain significance
rs7569789641:171,303,625C/Auncertain significance
rs7569517061:171,303,677G/Auncertain significance
rs7499838421:171,303,797A/Tuncertain significance
rs455997421:171,303,836G/Alikely benign
rs10116054421:171,303,860G/Auncertain significance
rs3690132321:171,303,905A/Guncertain significance
rs454454971:171,306,520A/Gbenign
rs746079871:171,310,562A/Clikely benign
rs7625310631:171,310,602T/Cuncertain significance
rs7795478881:171,310,680A/Cuncertain significance
rs25260742541:171,310,718C/Tuncertain significance
rs1437138561:171,310,775A/Guncertain significance
rs7587097021:171,310,779C/Tuncertain significance
rs9635359461:171,310,839A/Guncertain significance
rs756616711:171,310,901T/Cbenign
rs2002621641:171,310,959T/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.