FMOD

fibromodulin

Summary

Fibromodulin belongs to the family of small interstitial proteoglycans. The encoded protein possesses a central region containing leucine-rich repeats with 4 keratan sulfate chains, flanked by terminal domains containing disulphide bonds. Owing to the interaction with type I and type II collagen fibrils and in vitro inhibition of fibrillogenesis, the encoded protein may play a role in the assembly of extracellular matrix. It may also regulate TGF-beta activities by sequestering TGF-beta into the extracellular matrix. Sequence variations in this gene may be associated with the pathogenesis of high myopia. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jun 2013]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1483114171:203,311,542C/Guncertain significance
rs1494955241:203,316,423T/Guncertain significance
rs2019696141:203,316,507G/Tuncertain significance
rs25266292131:203,316,564T/Cuncertain significance
rs3691360711:203,316,578C/Tuncertain significance
rs1397301401:203,316,600C/Guncertain significance
rs7703446331:203,316,618C/Tuncertain significance
rs7526096741:203,316,624C/Tuncertain significance
rs13413933431:203,316,651A/Guncertain significance
rs7461256711:203,316,684G/Tuncertain significance
rs1433908041:203,316,692C/Tuncertain significance
rs7639441241:203,316,732G/Auncertain significance
rs5482360441:203,316,830C/Tuncertain significance
rs1453221781:203,316,872C/Tuncertain significance
rs7805922411:203,316,960C/Tuncertain significance
rs7454058731:203,316,962A/Guncertain significance
rs25266311401:203,316,982G/Tuncertain significance
rs3775794361:203,316,987C/Tuncertain significance
rs3693867581:203,317,000C/Guncertain significance
rs2001312961:203,317,029C/Tuncertain significance
rs7688403291:203,317,107T/Guncertain significance
rs2003926001:203,317,128A/Guncertain significance
rs7746704631:203,317,158C/Tuncertain significance
rs25266322291:203,317,173A/Cuncertain significance
rs7734780791:203,317,176C/Tuncertain significance
rs14774209331:203,317,185C/Guncertain significance
rs1379500071:203,317,203C/Tuncertain significance
rs7609524451:203,317,238G/Cuncertain significance
rs13419821791:203,317,239G/Auncertain significance
rs7558221951:203,317,248C/Guncertain significance
rs7722657641:203,317,281C/Tuncertain significance
rs25266330451:203,317,308G/Tuncertain significance
rs1465645231:203,317,394T/Cuncertain significance
rs5648184281:203,319,479C/G
rs42465491:203,321,095G/T
rs49712531:203,321,414A/C

Gene information from NCBI Gene. Variant classifications from ClinVar.