GALNT7

polypeptide N-acetylgalactosaminyltransferase 7

Summary

This gene encodes GalNAc transferase 7, a member of the GalNAc-transferase family. The enzyme encoded by this gene controls the initiation step of mucin-type O-linked protein glycosylation and transfer of N-acetylgalactosamine to serine and threonine amino acid residues. This enzyme is a type II transmembrane protein and shares common sequence motifs with other family members. Unlike other family members, this enzyme shows exclusive specificity for partially GalNAc-glycosylated acceptor substrates and shows no activity with non-glycosylated peptides. This protein may function as a follow-up enzyme in the initiation step of O-glycosylation. [provided by RefSeq, Jul 2008]

Known Variants26 total

rsidPosition (GRCh37)AllelesClassClinVar
rs131162704:174,132,985T/C
rs131252404:174,151,619T/G
rs7503136124:174,169,237T/Cuncertain significance
rs25324118284:174,169,246A/Guncertain significance
rs13112914844:174,169,281A/Tuncertain significance
rs3772629414:174,169,296C/Tuncertain significance
rs12195576894:174,169,401G/Auncertain significance
rs799677114:174,169,569G/Auncertain significance
rs7587069624:174,169,584C/Guncertain significance
rs13035785244:174,169,589A/Cuncertain significance
rs1468993884:174,213,302G/Auncertain significance
rs13116166814:174,213,374C/Guncertain significance
rs7466659394:174,216,554A/Tuncertain significance
rs25325639594:174,216,588A/Cuncertain significance
rs7535697234:174,219,289T/Cuncertain significance
rs25325753554:174,219,438G/Cuncertain significance
rs351777444:174,223,282T/Cbenign
rs1500132234:174,235,170G/Auncertain significance
rs617411584:174,235,180G/Tbenign
rs14240295604:174,235,190C/Auncertain significance
rs7746692984:174,235,206C/Tuncertain significance
rs7644512494:174,235,224G/Auncertain significance
rs1448739134:174,235,304C/Amissense variant
rs1817921314:174,238,804C/Guncertain significance
rs14009872114:174,239,673G/Tuncertain significance
rs7550051664:174,242,828C/Tlikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.