GGPS1

geranylgeranyl diphosphate synthase 1

Summary

This gene is a member of the prenyltransferase family and encodes a protein with geranylgeranyl diphosphate (GGPP) synthase activity. The enzyme catalyzes the synthesis of GGPP from farnesyl diphosphate and isopentenyl diphosphate. GGPP is an important molecule responsible for the C20-prenylation of proteins and for the regulation of a nuclear hormone receptor. Alternate transcriptional splice variants, both protein-coding and non-protein-coding, have been found for this gene. [provided by RefSeq, Sep 2010]

Known Variants19 total

rsidPosition (GRCh37)AllelesClassClinVar
rs5650086181:235,489,621A/G
rs108026241:235,494,971A/Gupstream gene variant
rs1160887031:235,498,377G/Aupstream gene variant
rs16758310661:235,498,622C/Tuncertain significance
rs11573119401:235,498,623C/Tuncertain significance
rs14740576751:235,498,628A/Guncertain significance
rs8979433671:235,505,354A/Guncertain significance
rs3732000671:235,505,420C/Auncertain significance
rs10128437951:235,505,453A/Guncertain significance
rs13818234371:235,505,584G/Auncertain significance
rs2022283891:235,505,780G/Auncertain significance
rs1474354391:235,505,911A/Guncertain significance
rs25282610421:235,505,948G/Auncertain significance
rs25282610651:235,505,954T/Glikely pathogenic
rs21033516931:235,505,960A/Gpathogenic
rs7725823961:235,505,965C/Gpathogenic
rs12624028791:235,505,966G/Aconflicting classifications of pathogenicity
rs16760879051:235,505,972C/Auncertain significance
rs21033518131:235,506,038T/Gpathogenic

Gene information from NCBI Gene. Variant classifications from ClinVar.