GGT5

gamma-glutamyltransferase 5

Summary

This gene is a member of the gamma-glutamyl transpeptidase gene family, and some reports indicate that it is capable of cleaving the gamma-glutamyl moiety of glutathione. The protein encoded by this gene is synthesized as a single, catalytically-inactive polypeptide, that is processed post-transcriptionally to form a heavy and light subunit, with the catalytic activity contained within the small subunit. The encoded enzyme is able to convert leukotriene C4 to leukotriene D4, but appears to have distinct substrate specificity compared to gamma-glutamyl transpeptidase. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Oct 2014]

Known Variants73 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14950889322:24,615,951G/Auncertain significance
rs53222906022:24,615,979C/Tuncertain significance
rs75690676422:24,616,033A/Cuncertain significance
rs960825322:24,617,380G/Aintron variant
rs728627622:24,618,874T/Cintron variant
rs15036970122:24,618,962G/Aintron variant
rs37273241022:24,620,974T/Clikely benign
rs251736945222:24,621,000G/Cuncertain significance
rs77345065922:24,621,023C/Tuncertain significance
rs123144366822:24,621,037C/Tuncertain significance
rs75800550022:24,621,074C/Tuncertain significance
rs77123544122:24,621,314G/Auncertain significance
rs102680137322:24,621,319C/Tuncertain significance
rs54244043522:24,621,364A/Clikely benign
rs7527322222:24,621,540C/Tbenign
rs37482866722:24,621,553C/Tuncertain significance
rs20007393022:24,621,586T/Cuncertain significance
rs251738221222:24,622,071A/Cuncertain significance
rs53102150022:24,622,109C/Tlikely benign
rs75565316422:24,622,110G/Auncertain significance
rs76818728722:24,622,121G/Cuncertain significance
rs7387904322:24,622,124G/Abenign
rs55177850622:24,622,135C/Tuncertain significance
rs37234946822:24,622,177C/Tuncertain significance
rs14945686822:24,622,188C/Tconflicting classifications of pathogenicity
rs75432363422:24,622,225G/Auncertain significance
rs134233296322:24,622,632C/Auncertain significance
rs251738925122:24,622,633C/Tuncertain significance
rs251738943622:24,622,645C/Guncertain significance
rs960825522:24,623,137T/Cintron variant
rs2876543422:24,624,011T/Cintron variant
rs961256922:24,624,035C/T
rs13939734522:24,624,488A/Gintron variant
rs3450510422:24,624,609A/Gintron variant
rs75747039322:24,627,402G/Auncertain significance
rs13927381622:24,627,457C/Tuncertain significance
rs76874941622:24,627,486G/Auncertain significance
rs20051911622:24,628,014C/Asplice region variant
rs251742573622:24,628,052C/Auncertain significance
rs14509391522:24,628,062C/Tbenign
rs141912665322:24,628,076C/Tuncertain significance
rs251742641722:24,628,100C/Tuncertain significance
rs131334384322:24,628,151G/Tuncertain significance
rs7339631222:24,628,161G/Tuncertain significance
rs76929702022:24,628,167G/Cuncertain significance
rs76535495522:24,628,792G/Auncertain significance
rs14696982122:24,628,819G/Auncertain significance
rs204798726922:24,628,857G/Tuncertain significance
rs117075184822:24,628,912A/Tuncertain significance
rs74793457322:24,628,920C/Tuncertain significance
rs98933741622:24,628,921G/Auncertain significance
rs37320943722:24,628,929C/Tuncertain significance
rs77553702822:24,628,933G/Cuncertain significance
rs76884226422:24,628,942C/Tuncertain significance
rs7541365622:24,629,461G/Tbenign
rs14163497222:24,629,489G/Auncertain significance
rs76826883122:24,629,889A/Guncertain significance
rs14334675622:24,629,905C/Tuncertain significance
rs20007173322:24,629,911T/Clikely benign
rs89462172222:24,629,926C/Tuncertain significance
rs37531455422:24,629,928G/Auncertain significance
rs75060200422:24,629,929C/Tuncertain significance
rs74987243922:24,629,944C/Guncertain significance
rs11262494722:24,631,321C/Tintron variant
rs575182022:24,635,839G/C
rs18331673322:24,636,358T/Cregulatory region variant
rs76296895522:24,640,549C/Tuncertain significance
rs127060118222:24,640,567G/Auncertain significance
rs78074348422:24,640,579G/Cuncertain significance
rs75303214422:24,640,618C/Auncertain significance
rs130103187322:24,640,630C/Tlikely benign
rs146717300322:24,640,638G/Auncertain significance
rs204842626222:24,640,639C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.