GM2A

ganglioside GM2 activator

Summary

This gene encodes a small glycolipid transport protein which acts as a substrate specific co-factor for the lysosomal enzyme beta-hexosaminidase A. Beta-hexosaminidase A, together with GM2 ganglioside activator, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Mutations in this gene result in GM2-gangliosidosis type AB or the AB variant of Tay-Sachs disease. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Nov 2009]

Known Variants189 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1136078605:150,632,278G/Aregulatory region variant
rs1165940225:150,632,334C/Tbenign
rs17536175465:150,632,674T/Cuncertain significance
rs22770285:150,632,676G/Abenign
rs17536180215:150,632,695C/Guncertain significance
rs1449325945:150,632,734G/Abenign
rs3716288125:150,632,771C/Guncertain significance
rs7755850625:150,632,781C/Tlikely pathogenic
rs5622495265:150,632,782A/Guncertain significance
rs7626766675:150,632,788T/Auncertain significance
rs5574614695:150,632,790A/Tuncertain significance
rs7592490025:150,632,791T/Cuncertain significance
rs7523239075:150,632,801C/Tlikely benign
rs1438679535:150,632,810C/Tlikely benign
rs14017554765:150,632,813C/Tlikely benign
rs17536221455:150,632,814C/Tuncertain significance
rs3741611705:150,632,816G/Alikely benign
rs10487195:150,632,832G/Abenign
rs7802783675:150,632,834C/Glikely benign
rs10268354355:150,632,836C/Tuncertain significance
rs283659945:150,632,855A/Tlikely benign
rs3684433645:150,632,862A/Guncertain significance
rs412905755:150,633,108A/Cbenign
rs1167892935:150,637,238C/Aregulatory region variant
rs168385:150,639,162G/Cbenign
rs1534765:150,639,224A/Tbenign
rs7517728815:150,639,298C/Tlikely benign
rs25317458385:150,639,299T/Clikely benign
rs3691067535:150,639,301C/Tlikely benign
rs3762113445:150,639,308G/Clikely benign
rs25317458815:150,639,318A/Glikely benign
rs15820703765:150,639,319T/Cuncertain significance
rs3712964035:150,639,324G/Tuncertain significance
rs14279278935:150,639,332G/Auncertain significance
rs1132717405:150,639,360G/Alikely benign
rs15820704355:150,639,363G/Alikely benign
rs7612688105:150,639,371C/Auncertain significance
rs1475119205:150,639,372G/Alikely benign
rs12691016845:150,639,373G/Auncertain significance
rs1048938975:150,639,394G/Tstop gainedpathogenic
rs7308821965:150,639,398C/Tmissense variantpathogenic
rs7553827275:150,639,406A/Tuncertain significance
rs7677811095:150,639,407T/Cuncertain significance
rs1534775:150,639,409A/Gmissense variantbenign
rs7457992775:150,639,411C/Tlikely benign
rs2018296505:150,639,412G/Auncertain significance
rs1411992545:150,639,416C/Guncertain significance
rs25317462875:150,639,418G/Auncertain significance
rs7685239265:150,639,429C/Tlikely benign
rs8930361335:150,639,437T/Cuncertain significance
rs1534785:150,639,439A/Gmissense variantbenign
rs7692612535:150,639,440T/Cuncertain significance
rs21140325245:150,639,441G/Auncertain significance
rs7667384465:150,639,486G/Alikely benign
rs12708088885:150,639,487G/Alikely benign
rs22770295:150,639,621C/Gbenign
rs1534795:150,639,778G/Abenign
rs65798455:150,642,265A/Gintron variant
rs7694923875:150,646,277A/Tlikely benign
rs7728627615:150,646,279T/Glikely benign
rs21272405775:150,646,286T/Clikely benign
rs10575190225:150,646,290A/Tpathogenic
rs1390149245:150,646,292G/Cuncertain significance
rs1439999545:150,646,302T/Guncertain significance
rs2010665685:150,646,309G/Alikely benign
rs7514175465:150,646,344G/Auncertain significance
rs14438800215:150,646,356T/Cuncertain significance
rs9071963145:150,646,363C/Tlikely benign
rs5877794055:150,646,381pathogenic
rs7772505935:150,646,390G/Clikely benign
rs1451114695:150,646,394G/Cuncertain significance
rs25317565555:150,646,412G/Alikely pathogenic
rs15616201305:150,646,427G/Auncertain significance
rs25317566135:150,646,429G/Alikely benign
rs7610845525:150,646,436C/Tuncertain significance
rs7691690885:150,646,437G/Alikely benign
rs7621316295:150,646,443A/Tuncertain significance
rs1378527975:150,646,460T/Cmissense variantpathogenic
rs11747355585:150,646,461G/Alikely pathogenic
rs7776633335:150,646,485A/Tlikely benign
rs20757825:150,646,647T/Cbenign
rs68617665:150,646,736C/Tbenign
rs20757835:150,646,780A/Cbenign
rs1836970135:150,646,835C/Tlikely benign
rs25317574155:150,646,843T/Alikely pathogenic
rs17539059905:150,646,844G/Auncertain significance
rs13446779395:150,646,845G/Alikely benign
rs7536091685:150,646,850C/Tlikely benign
rs25317574405:150,646,851C/Tlikely benign
rs7614114855:150,646,853G/Alikely benign
rs7579547705:150,646,858G/Auncertain significance
rs25317574615:150,646,859A/Tlikely benign
rs12677769335:150,646,875A/Cuncertain significance
rs12803528845:150,646,879G/Auncertain significance
rs7555697395:150,646,880C/Tlikely benign
rs617406025:150,646,888T/Cbenign
rs17539080175:150,646,897A/Tuncertain significance
rs10575190215:150,646,902G/Tstop gainedpathogenic
rs7744715125:150,646,922C/Glikely benign
rs7596237125:150,646,925C/Tlikely benign

Showing 100 of 189 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.