HACD4

3-hydroxyacyl-CoA dehydratase 4

Summary

Enables enzyme binding activity and very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase activity. Involved in fatty acid elongation and very long-chain fatty acid biosynthetic process. Located in endoplasmic reticulum. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants20 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7632139409:21,007,058G/Cuncertain significance
rs7782671059:21,007,115A/Tuncertain significance
rs10088359809:21,008,038G/Cuncertain significance
rs11776025419:21,008,109G/Auncertain significance
rs24891161329:21,008,145G/Cuncertain significance
rs3731644039:21,011,609G/Auncertain significance
rs7488547879:21,011,633G/Cuncertain significance
rs125513419:21,014,628T/G
rs7775118549:21,015,945T/Cuncertain significance
rs12667576289:21,016,005G/Auncertain significance
rs7517984399:21,026,666C/Tlikely benign
rs7650574979:21,026,668G/Auncertain significance
rs3732734839:21,026,692C/Guncertain significance
rs2003295549:21,029,301A/Gsynonymous variant
rs24891481159:21,029,349A/Cuncertain significance
rs7741731979:21,029,350C/Guncertain significance
rs3769197139:21,029,358G/Cuncertain significance
rs12571722719:21,029,366A/Tuncertain significance
rs9858626309:21,031,583G/Tuncertain significance
rs12327629919:21,031,585C/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.