HAO2

hydroxyacid oxidase 2

Summary

This gene is one of three related genes that have 2-hydroxyacid oxidase activity. The encoded protein localizes to the peroxisome has the highest activity toward the substrate 2-hydroxypalmitate. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2014]

Known Variants30 total

rsidPosition (GRCh37)AllelesClassClinVar
rs22249951:119,923,531A/Cintron variant
rs7556980471:119,923,773G/Auncertain significance
rs1493933481:119,925,549G/Auncertain significance
rs3711855401:119,925,552C/Tuncertain significance
rs1997052141:119,925,554C/Tuncertain significance
rs3740521031:119,925,612T/Guncertain significance
rs413139951:119,925,632G/Tmissense variant
rs7481151721:119,925,653C/Tuncertain significance
rs25262601481:119,927,426T/Cuncertain significance
rs25262603891:119,927,450G/Auncertain significance
rs14028227181:119,927,452C/Guncertain significance
rs25262614561:119,927,540T/Auncertain significance
rs7616605551:119,927,544G/Cuncertain significance
rs14872895381:119,927,596G/Cuncertain significance
rs7504239371:119,927,629C/Auncertain significance
rs1400544261:119,929,273C/Tuncertain significance
rs11703111891:119,929,294G/Auncertain significance
rs7731419521:119,929,320A/Guncertain significance
rs7580594871:119,929,383G/Auncertain significance
rs9035282441:119,929,399A/Tuncertain significance
rs7776252571:119,929,404A/Guncertain significance
rs75288381:119,929,713A/Tintron variant
rs3717648431:119,934,734T/Cuncertain significance
rs7569323551:119,934,785A/Tuncertain significance
rs3757153561:119,934,803G/Auncertain significance
rs13064739831:119,934,848G/Tuncertain significance
rs14681733661:119,934,863G/Auncertain significance
rs2008299351:119,935,280A/Guncertain significance
rs1436705011:119,936,419G/Tuncertain significance
rs7751351791:119,936,435G/Alikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.