HOXD13

homeobox D13

Summary

This gene belongs to the homeobox family of genes. The homeobox genes encode a highly conserved family of transcription factors that play an important role in morphogenesis in all multicellular organisms. Mammals possess four similar homeobox gene clusters, HOXA, HOXB, HOXC and HOXD, located on different chromosomes, consisting of 9 to 11 genes arranged in tandem. This gene is one of several homeobox HOXD genes located in a cluster on chromosome 2. Deletions that remove the entire HOXD gene cluster or the 5' end of this cluster have been associated with severe limb and genital abnormalities. Mutations in this particular gene cause synpolydactyly. [provided by RefSeq, Jul 2008]

Known Variants81 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1850866752:176,953,289C/Tbenign
rs1156911652:176,957,201G/Cbenign
rs1131439792:176,957,230T/Abenign
rs729234242:176,957,519C/Alikely benign
rs1445770202:176,957,580G/Cbenign
rs13532214622:176,957,624C/Auncertain significance
rs5366395832:176,957,650G/Cmissense variantpathogenic
rs5551366842:176,957,659C/Tlikely benign
rs21053781062:176,957,674C/Guncertain significance
rs13510233042:176,957,735G/Cuncertain significance
rs16893466362:176,957,743G/Tuncertain significance
rs7571758602:176,957,753C/Tconflicting classifications of pathogenicity
rs11829196672:176,957,776A/Tuncertain significance
rs14432257612:176,957,782G/Cuncertain significance
rs16893476192:176,957,785G/Auncertain significance
rs7552839842:176,957,788C/Tuncertain significance
rs7601686662:176,957,820G/Cuncertain significance
rs25180532:176,957,822G/Abenign
rs5444498252:176,957,835G/Auncertain significance
rs7779261462:176,957,859G/Auncertain significance
rs1399954912:176,957,878C/Guncertain significance
rs7724795242:176,957,885G/Abenign
rs5626382002:176,957,908C/Tuncertain significance
rs1434877522:176,957,914C/Guncertain significance
rs3735464232:176,957,915G/Tbenign
rs2005144972:176,957,932A/Clikely benign
rs8788543432:176,957,941pathogenic
rs5598432972:176,957,973C/Tuncertain significance
rs9051296092:176,957,977C/Auncertain significance
rs7504126842:176,957,989C/Auncertain significance
rs24681527852:176,958,007A/Guncertain significance
rs8471952:176,958,011C/Tbenign
rs10185485422:176,958,067C/Tuncertain significance
rs21053787152:176,958,084C/Tuncertain significance
rs3718065212:176,958,092G/Tlikely benign
rs2000677742:176,958,118A/Gconflicting classifications of pathogenicity
rs7789784742:176,958,125C/Auncertain significance
rs12217156172:176,958,131A/Guncertain significance
rs16893596812:176,958,154C/Tuncertain significance
rs1489793532:176,958,159A/Glikely benign
rs14314722602:176,958,178C/Guncertain significance
rs14099301332:176,958,225G/Auncertain significance
rs7468542732:176,958,231G/Auncertain significance
rs1477207462:176,958,235A/Gbenign
rs21053790982:176,958,241A/Tuncertain significance
rs3676749212:176,958,292C/Guncertain significance
rs1219125412:176,958,301G/Tmissense variantpathogenic
rs5770164232:176,958,304A/Guncertain significance
rs16893658532:176,958,327G/Cuncertain significance
rs8788544002:176,958,360C/Tstop gainedpathogenic
rs14342577462:176,958,362G/Cuncertain significance
rs24681539672:176,958,399G/Auncertain significance
rs8860378312:176,958,400G/Apathogenic
rs796451622:176,958,450G/Tlikely benign
rs8471942:176,958,701A/Cbenign
rs729234252:176,958,962T/Cbenign
rs8471932:176,959,008A/Gbenign
rs8471922:176,959,079G/Abenign
rs7648384782:176,959,206pathogenic
rs24681556882:176,959,231G/Auncertain significance
rs7690846922:176,959,233C/Tlikely benign
rs1999820172:176,959,239C/Tlikely benign
rs2007505642:176,959,246C/Tstop gainedpathogenic
rs8788543442:176,959,260pathogenic
rs21053798192:176,959,285C/Auncertain significance
rs24681558152:176,959,310A/Guncertain significance
rs15535173462:176,959,338C/Guncertain significance
rs289330822:176,959,342C/Tmissense variantpathogenic
rs8792552652:176,959,343G/Amissense variantpathogenic
rs12057459042:176,959,348C/Tuncertain significance
rs7702268262:176,959,349G/Auncertain significance
rs13019277452:176,959,363A/Cuncertain significance
rs14320639932:176,959,364C/Glikely pathogenic
rs289288922:176,959,373C/Gmissense variantpathogenic
rs21053799072:176,959,378A/Guncertain significance
rs289288912:176,959,390A/Cmissense variantpathogenic
rs8759898422:176,959,399C/Amissense variantpathogenic
rs1048936352:176,959,400A/Gmissense variantpathogenic
rs3692169222:176,959,431C/Tlikely benign
rs7616793012:176,959,440C/Tlikely benign
rs729234262:176,959,769C/Tbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.