HSD17B6

hydroxysteroid 17-beta dehydrogenase 6

Summary

The protein encoded by this gene has both oxidoreductase and epimerase activities and is involved in androgen catabolism. The oxidoreductase activity can convert 3 alpha-adiol to dihydrotestosterone, while the epimerase activity can convert androsterone to epi-androsterone. Both reactions use NAD+ as the preferred cofactor. This gene is a member of the retinol dehydrogenase family. [provided by RefSeq, Aug 2013]

Known Variants27 total

rsidPosition (GRCh37)AllelesClassClinVar
rs89861112:57,163,316C/Tintron variant
rs14219875812:57,167,653C/Tlikely benign
rs37739195612:57,167,660C/Tlikely benign
rs76270628012:57,167,698G/Auncertain significance
rs37559817012:57,167,740C/Auncertain significance
rs75748275212:57,167,742G/Auncertain significance
rs20109841212:57,167,752C/Tuncertain significance
rs37517898212:57,167,778C/Guncertain significance
rs254789076012:57,167,806T/Cuncertain significance
rs98363745712:57,167,808G/Auncertain significance
rs37089854412:57,167,821C/Tuncertain significance
rs254789077712:57,167,828G/Cuncertain significance
rs14821184812:57,167,835G/Auncertain significance
rs14734447012:57,167,873G/Abenign
rs1045924712:57,171,516T/Cintron variant
rs14591420612:57,172,571G/Cintron variant
rs148074691812:57,175,766G/Auncertain significance
rs14947296012:57,175,769C/Guncertain significance
rs77159424112:57,175,896T/Cuncertain significance
rs1087692012:57,176,175C/G
rs76444769712:57,178,639G/Auncertain significance
rs77867571612:57,178,710A/Guncertain significance
rs76568398112:57,178,753C/Auncertain significance
rs75890044812:57,178,756C/Guncertain significance
rs14625346812:57,180,917A/Guncertain significance
rs13938817312:57,181,002C/Tuncertain significance
rs103375670612:57,181,074T/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.