HSPB1

heat shock protein family B (small) member 1

Summary

This gene encodes a member of the small heat shock protein (HSP20) family of proteins. In response to environmental stress, the encoded protein translocates from the cytoplasm to the nucleus and functions as a molecular chaperone that promotes the correct folding of other proteins. This protein plays an important role in the differentiation of a wide variety of cell types. Expression of this gene is correlated with poor clinical outcome in multiple human cancers, and the encoded protein may promote cancer cell proliferation and metastasis, while protecting cancer cells from apoptosis. Mutations in this gene have been identified in human patients with Charcot-Marie-Tooth disease and distal hereditary motor neuropathy. [provided by RefSeq, Aug 2017]

Known Variants272 total

rsidPosition (GRCh37)AllelesClassClinVar
rs28683717:75,930,759C/Gupstream gene variant
rs28683707:75,930,800G/Aupstream gene variant
rs69633107:75,931,676C/Tlikely benign
rs1174586997:75,931,729G/Clikely benign
rs8860624467:75,931,901G/Tuncertain significance
rs5531275137:75,931,908G/Tconflicting classifications of pathogenicity
rs357599787:75,931,974C/Tlikely benign
rs359071747:75,931,984C/Tbenign
rs1996029567:75,932,011C/Tlikely benign
rs7562609297:75,932,015G/Aconflicting classifications of pathogenicity
rs9484692247:75,932,025C/Tlikely benign
rs3728334367:75,932,026C/Tconflicting classifications of pathogenicity
rs2001907227:75,932,030A/Cuncertain significance
rs11732423137:75,932,032G/Aconflicting classifications of pathogenicity
rs7480033517:75,932,036G/Auncertain significance
rs775867677:75,932,038G/Alikely benign
rs7487303747:75,932,040G/Auncertain significance
rs10493247:75,932,045G/Aconflicting classifications of pathogenicity
rs7738648167:75,932,046T/Cuncertain significance
rs115471647:75,932,047C/Glikely benign
rs15636516987:75,932,048C/Tconflicting classifications of pathogenicity
rs14053598147:75,932,049C/Gconflicting classifications of pathogenicity
rs7599982007:75,932,050C/Tlikely benign
rs2017696687:75,932,053C/Tlikely benign
rs12324137267:75,932,056G/Tlikely benign
rs7722167587:75,932,058T/Auncertain significance
rs1997126007:75,932,062G/Clikely benign
rs1453698597:75,932,065G/Tlikely benign
rs14751844547:75,932,066G/Auncertain significance
rs7505881417:75,932,068C/Tlikely benign
rs7670458477:75,932,069C/Tuncertain significance
rs115471637:75,932,073G/Auncertain significance
rs7808787807:75,932,074C/Auncertain significance
rs9731262667:75,932,076G/Auncertain significance
rs18030144177:75,932,081C/Auncertain significance
rs25361489767:75,932,087C/Auncertain significance
rs18030146287:75,932,089C/Tuncertain significance
rs21171577927:75,932,095G/Cuncertain significance
rs14141487927:75,932,099C/Auncertain significance
rs3741725707:75,932,104T/Guncertain significance
rs21171578257:75,932,106G/Auncertain significance
rs12217012697:75,932,107C/Auncertain significance
rs3676623947:75,932,109G/Cconflicting classifications of pathogenicity
rs7786720477:75,932,113C/Tlikely benign
rs7717097777:75,932,118A/Cuncertain significance
rs7757282297:75,932,120C/Guncertain significance
rs7693490927:75,932,123G/Tuncertain significance
rs7772612107:75,932,124C/Tuncertain significance
rs7620328467:75,932,128C/Tlikely benign
rs15546144327:75,932,129G/Auncertain significance
rs7651977247:75,932,137C/Glikely benign
rs7630980347:75,932,138C/Tuncertain significance
rs3721976307:75,932,139G/Clikely benign
rs14396649347:75,932,141C/Auncertain significance
rs5573271657:75,932,145C/Tpathogenic
rs7525557647:75,932,146G/Alikely benign
rs7472957247:75,932,147G/Tuncertain significance
rs7558903277:75,932,148A/Tuncertain significance
rs12775698257:75,932,149G/Alikely benign
rs13934049717:75,932,150G/Auncertain significance
rs115471677:75,932,152G/Alikely benign
rs8960044297:75,932,155G/Apathogenic
rs13466003667:75,932,156T/Cuncertain significance
rs9502342867:75,932,157C/Guncertain significance
rs7640713047:75,932,158G/Alikely benign
rs7537477427:75,932,163G/Auncertain significance
rs14369257947:75,932,165T/Guncertain significance
rs7571806087:75,932,167A/Glikely benign
rs7783117767:75,932,168G/Auncertain significance
rs5466992217:75,932,171G/Auncertain significance
rs25361491897:75,932,173C/Alikely benign
rs14042123067:75,932,178G/Tuncertain significance
rs14081599227:75,932,181G/Auncertain significance
rs7691181157:75,932,182G/Aconflicting classifications of pathogenicity
rs14485172697:75,932,184C/Guncertain significance
rs3752442097:75,932,187G/Aconflicting classifications of pathogenicity
rs7486966287:75,932,188C/Tlikely benign
rs7702852357:75,932,191C/Tlikely benign
rs18030213547:75,932,192G/Cuncertain significance
rs12481579357:75,932,197C/Tlikely benign
rs18030218857:75,932,198C/Tuncertain significance
rs8871521837:75,932,200C/Tlikely benign
rs8922587457:75,932,203G/Clikely benign
rs7630844607:75,932,204C/Tuncertain significance
rs9967027717:75,932,206C/Tlikely benign
rs617512177:75,932,207C/Tlikely benign
rs1120750847:75,932,208C/Guncertain significance
rs7745351757:75,932,209C/Tlikely benign
rs7605064717:75,932,212C/Tlikely benign
rs10647966027:75,932,213G/Auncertain significance
rs11673222587:75,932,218C/Tlikely benign
rs18030237087:75,932,219G/Auncertain significance
rs18030238687:75,932,221G/Cuncertain significance
rs25361493857:75,932,225C/Tuncertain significance
rs7639099057:75,932,227C/Tlikely benign
rs7535850867:75,932,228G/Auncertain significance
rs7571585147:75,932,231G/Cuncertain significance
rs15546144627:75,932,233G/Clikely benign
rs14412455087:75,932,237G/Auncertain significance
rs7499636537:75,932,239G/Aconflicting classifications of pathogenicity

Showing 100 of 272 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.