IBSP

integrin binding sialoprotein

Summary

The protein encoded by this gene is a major structural protein of the bone matrix. It constitutes approximately 12% of the noncollagenous proteins in human bone and is synthesized by skeletal-associated cell types, including hypertrophic chondrocytes, osteoblasts, osteocytes, and osteoclasts. The only extraskeletal site of its synthesis is the trophoblast. This protein binds to calcium and hydroxyapatite via its acidic amino acid clusters, and mediates cell attachment through an RGD sequence that recognizes the vitronectin receptor. [provided by RefSeq, Jul 2008]

Known Variants15 total

rsidPosition (GRCh37)AllelesClassClinVar
rs26162624:88,723,210G/C
rs1140095644:88,723,842C/Tlikely benign
rs9584761964:88,727,279T/Guncertain significance
rs7478919034:88,731,792C/Tuncertain significance
rs7489544904:88,732,595G/Auncertain significance
rs2004054814:88,732,603C/Auncertain significance
rs9131382124:88,732,604G/Auncertain significance
rs7642880094:88,732,688G/Auncertain significance
rs10546274:88,732,692G/Amissense variant
rs7561459394:88,732,698A/Tuncertain significance
rs7462064064:88,732,760G/Cuncertain significance
rs170131814:88,732,763A/Gmissense variant
rs24761059054:88,732,931T/Cuncertain significance
rs24761059864:88,732,976T/Cuncertain significance
rs7812634794:88,733,054C/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.