KASH5

KASH domain containing 5

Summary

Predicted to enable dynein complex binding activity. Predicted to be involved in several processes, including cytoskeleton organization; homologous chromosome segregation; and spindle localization. Predicted to act upstream of or within several processes, including double-strand break repair via homologous recombination; meiotic telomere clustering; and spermatogenesis. Predicted to be located in chromosome; membrane; and nuclear envelope. Predicted to be part of meiotic nuclear membrane microtubule tethering complex. Predicted to be active in chromosome; meiotic spindle pole; and nuclear outer membrane. Implicated in primary ovarian insufficiency and spermatogenic failure 88. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants39 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14774579419:49,891,469C/Tregulatory region variant
rs20103208019:49,894,178C/Tuncertain significance
rs76981292019:49,897,747C/Tuncertain significance
rs36772805119:49,897,813G/Auncertain significance
rs121598409519:49,898,381A/Guncertain significance
rs251380399119:49,898,390C/Tuncertain significance
rs19197309119:49,898,404A/Glikely benign
rs139117044419:49,898,426A/Guncertain significance
rs20189066019:49,898,431C/Tuncertain significance
rs251380483119:49,898,516T/Cuncertain significance
rs78030243619:49,898,545C/Tuncertain significance
rs125432952619:49,899,045G/Auncertain significance
rs77770515819:49,899,049C/Tuncertain significance
rs76654057219:49,899,063G/Tuncertain significance
rs57344413719:49,901,358G/Tuncertain significance
rs251381532519:49,901,361T/Cpathogenic
rs37123754319:49,902,391C/Tuncertain significance
rs94268895619:49,902,392G/Auncertain significance
rs20072379719:49,902,399G/Alikely pathogenic
rs56223201619:49,910,197G/Auncertain significance
rs37099602919:49,910,521C/Tuncertain significance
rs88623628519:49,910,525T/Cuncertain significance
rs37022661319:49,912,278G/Auncertain significance
rs136567277119:49,912,282C/Auncertain significance
rs76717240419:49,912,502C/Tuncertain significance
rs19969441219:49,912,510G/Alikely benign
rs18857286419:49,912,545G/Apathogenic
rs37659812919:49,913,084G/Clikely benign
rs75031630019:49,913,124G/Auncertain significance
rs103084908919:49,913,128G/Auncertain significance
rs54686427619:49,913,934G/A
rs76785846319:49,920,280C/Alikely benign
rs20186275819:49,920,303G/Alikely benign
rs75417364419:49,920,426C/Tuncertain significance
rs127669567219:49,920,498C/Tuncertain significance
rs14541298119:49,920,634G/Cuncertain significance
rs143936517719:49,920,682T/Apathogenic
rs76256163019:49,920,705C/Tuncertain significance
rs94290468819:49,920,706C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.