KATNAL1

katanin catalytic subunit A1 like 1

Summary

Enables identical protein binding activity and microtubule severing ATPase activity. Involved in microtubule severing. Located in cytosol; microtubule cytoskeleton; and mitochondrion. Part of katanin complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants23 total

rsidPosition (GRCh37)AllelesClassClinVar
rs254186663013:30,782,775C/Tuncertain significance
rs187337245413:30,782,777T/Auncertain significance
rs203199813:30,783,452G/T
rs128580503113:30,784,507T/Auncertain significance
rs76223111913:30,784,568C/Tlikely benign
rs77245569913:30,784,573C/Guncertain significance
rs14694493713:30,791,405C/G
rs96064276213:30,801,562T/Cuncertain significance
rs254189097013:30,801,627C/Tuncertain significance
rs187599099413:30,804,640C/Auncertain significance
rs75073922713:30,804,731C/Tuncertain significance
rs76814459713:30,805,518G/Auncertain significance
rs74780635313:30,814,598T/Cuncertain significance
rs18247177213:30,814,641T/Cuncertain significance
rs37756609113:30,815,209C/Auncertain significance
rs37722224013:30,829,609T/Clikely benign
rs20059685413:30,829,726T/Cuncertain significance
rs955188113:30,829,740C/Guncertain significance
rs76294310413:30,854,218G/Tuncertain significance
rs250020945913:30,854,320C/Auncertain significance
rs250022497713:30,857,783T/Auncertain significance
rs955055113:30,882,197G/Aregulatory region variant
rs476982413:30,883,339C/Tupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.