KCNC2

potassium voltage-gated channel subfamily C member 2

Summary

The Shaker gene family of Drosophila encodes components of voltage-gated potassium channels and is comprised of four subfamilies. Based on sequence similarity, this gene is similar to one of these subfamilies, namely the Shaw subfamily. The protein encoded by this gene belongs to the delayed rectifier class of channel proteins and is an integral membrane protein that mediates the voltage-dependent potassium ion permeability of excitable membranes. Several transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, May 2012]

Known Variants56 total

rsidPosition (GRCh37)AllelesClassClinVar
rs20201817112:75,436,121G/Auncertain significance
rs20133916412:75,436,154T/Auncertain significance
rs1050667712:75,439,487G/T
rs15124823112:75,441,944C/Guncertain significance
rs37234167112:75,442,028C/Auncertain significance
rs74907823312:75,442,078A/Tuncertain significance
rs92359086912:75,444,187A/Tuncertain significance
rs20166804112:75,444,193C/Tuncertain significance
rs188104409812:75,444,205C/Auncertain significance
rs254784307312:75,444,218C/Guncertain significance
rs117692110912:75,444,259C/Auncertain significance
rs254784359012:75,444,361T/Guncertain significance
rs188106603512:75,444,367A/Tlikely pathogenic
rs213694335312:75,444,374C/Gpathogenic
rs188106686112:75,444,377G/Aconflicting classifications of pathogenicity
rs213694341412:75,444,380C/Auncertain significance
rs254784363912:75,444,382G/Auncertain significance
rs213694375712:75,444,476T/Cpathogenic
rs254784386312:75,444,493G/Auncertain significance
rs213694409312:75,444,572T/Clikely pathogenic
rs126022297012:75,444,575C/Tlikely pathogenic
rs254784420012:75,444,622A/Gpathogenic
rs14943346012:75,444,639A/Glikely benign
rs188109185612:75,444,640A/Cuncertain significance
rs37459611712:75,444,668G/Cuncertain significance
rs213694468412:75,444,733C/Tpathogenic
rs254784445612:75,444,784C/Tuncertain significance
rs37184658012:75,445,006T/Cuncertain significance
rs37658713412:75,445,063A/Guncertain significance
rs20191889012:75,445,076A/Glikely benign
rs18723723012:75,451,604C/Tintron variant
rs730507912:75,464,411A/Tintron variant
rs206140612:75,494,517G/Aintron variant
rs7440268212:75,598,315A/Gintron variant
rs254816714912:75,601,127G/Auncertain significance
rs20172134812:75,601,178C/Tuncertain significance
rs119979463112:75,601,192C/Tuncertain significance
rs20031536412:75,601,240A/Guncertain significance
rs20142836312:75,601,248G/Clikely benign
rs213782778312:75,601,265C/Apathogenic
rs254816819212:75,601,277C/Tlikely pathogenic
rs254816842812:75,601,325C/Guncertain significance
rs75858529312:75,601,334C/Tuncertain significance
rs213782844512:75,601,360T/Cpathogenic
rs6173571212:75,601,389G/Apathogenic
rs254816878812:75,601,403C/Auncertain significance
rs254816893512:75,601,442G/Auncertain significance
rs138835600512:75,601,465C/Auncertain significance
rs20030915112:75,601,481G/Tuncertain significance
rs77905298512:75,601,499C/Tuncertain significance
rs55449600812:75,601,517C/Tuncertain significance
rs254816935112:75,601,525C/Auncertain significance
rs731112212:75,601,540C/Alikely benign
rs76691191012:75,601,594G/Auncertain significance
rs14657614912:75,601,665G/Abenign
rs131111301112:75,601,740C/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.